View source for Eisenmenger’s syndrome diagnostic study of choice

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{{Template:Eisenmenger's syndrome}}
{{CMG}}'''; Associate Editor(s)-In-Chief:''' {{AIA}}, [[Priyamvada Singh|Priyamavada Singh, MBBS]] [mailto:psingh13579@gmail.com], [[Kristin Feeney|Kristin Feeney, B.S.]] [mailto:kfeeney@elon.edu]

==Overview==

==2018 ACC/AHA Guidelines for the Management of Adults With Congenital Heart Disease (DO NOT EDIT)<ref name="pmid30586767">Stout KK, Daniels CJ, Aboulhosn JA, Bozkurt B, Broberg CS, Colman JM et al. (2019) [https://www.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pubmed&retmode=ref&cmd=prlinks&id=30586767 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines.] ''Circulation'' 139 (14):e698-e800. [http://dx.doi.org/10.1161/CIR.0000000000000603 DOI:10.1161/CIR.0000000000000603] PMID: [https://pubmed.gov/30586767 30586767]</ref>==
{| class="wikitable"
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| colspan="1" style="text-align:center; background:LightGreen"|[[ACC AHA guidelines classification scheme#Classification of Recommendations|Class I]]
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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''1.''' Care of adult patients with [[CHD]]-related PAH should be performed in centers that have shared expertise and training in both ACHD and [[PAH]]. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''2.''' The evaluation of all ACHD patients with suspected PAH should include [[noninvasive]] assessment of [[cardiovascular]] [[anatomy]] and potential [[shunting]], as detailed below:<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''a.''' [[Pulse oximetry]], with and without administration of supplemental oxygen, as appropriate. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''b.''' [[Chest x-ray]]. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''c.''' [[ECG]]. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

|-
| bgcolor="LightGreen"|<nowiki>"</nowiki>'''d.''' Diagnostic cardiovascular imaging via [[TTE]], [[TEE]], [[MRI]], or [[CT]] as appropriate. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''e.''' [[Complete blood count]] and [[nuclear]] lung [[scintigraphy]]. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''3.''' If PAH is identified but its causes are not fully recognized, additional testing should include the following:<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''a.''' [[Pulmonary function test]]s with volumes and [[diffusion capacity]] (diffusing capacity of the lung for [[carbon monoxide]]). ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''b.''' [[Pulmonary embolism]]-protocol [[CT]] with parenchymal lung windows. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''c.''' Additional testing as appropriate to rule out contributing causes of PAH. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>

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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''d.''' [[Cardiac catheterization]] at least once, with potential for [[vasodilator]] testing or anatomic intervention, at a center with expertise in catheterization, PAH, and management of CHD-PAH. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>
|}

{| class="wikitable"
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| colspan="1" style="text-align:center; background:LemonChiffon"| [[ACC AHA guidelines classification scheme#Classification of Recommendations|Class IIa]]
|-
| bgcolor="LemonChiffon"|<nowiki>"</nowiki>'''1.''' It is reasonable to include a 6-minute walk test or similar nonmaximal cardiopulmonary [[exercise test]] as part of the functional assessment of patients with [[CHD]]-[[PAH]]. ''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])''<nowiki>"</nowiki>
|}

==References==
{{reflist|2}}

[[Category:Cardiology]]
[[Category:Congenital heart disease]]
[[Category:Pediatrics]]
[[Category:Disease]]