Fibromatosis: Difference between revisions
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{{SK}} Fibromyxoma; myxofibroma; musculoaponeurotic fibromatosis | |||
==Overview== | ==Overview== | ||
The term '''fibromatosis''' refers to a group of [[benign]] [[soft tissue]] [[tumor]]s which have certain characteristics in common, including absence of cytologic and clinical [[malignant]] features, a [[histology]] consistent with proliferation of well-differentiated [[fibroblasts]], an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence. Other names include "musculoaponeurotic fibromatosis," referring to the tendency of these tumors to be adjacent to and infiltrating deep [[skeletal muscle]], and "desmoid tumor," an obsolete term which more specifically refers to the occurrence of these tumors in the [[abdominal wall]] of a pregnant woman. Treatment includes prompt radical excision with a wide margin and/or [[Radiation therapy|radiation]]. Despite the local infiltrative and aggressive behavior of these tumors, mortality secondary to these tumors is minimal to nonexistent. | The term '''fibromatosis''' refers to a group of [[benign]] [[soft tissue]] [[tumor]]s which have certain characteristics in common, including absence of cytologic and clinical [[malignant]] features, a [[histology]] consistent with proliferation of well-differentiated [[fibroblasts]], an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence. Other names include "musculoaponeurotic fibromatosis," referring to the tendency of these tumors to be adjacent to and infiltrating deep [[skeletal muscle]], and "desmoid tumor," an obsolete term which more specifically refers to the occurrence of these tumors in the [[abdominal wall]] of a pregnant woman. Treatment includes prompt radical excision with a wide margin and/or [[Radiation therapy|radiation]]. Despite the local infiltrative and aggressive behavior of these tumors, mortality secondary to these tumors is minimal to nonexistent. | ||
==Classification== | |||
Subtypes of fibromatosis include juvenile fibromatosis, fibromatosis colli, infantile digital fibromatosis, infantile myofibromatosis, lipofibromatosis, fibromatosis hyalinica multiplex, penile fibromatosis (Peyronie's disease), and palmar fibromatosis (Dupuytren's contracture). Multiple fibromatoses are seen in [[Gardner's syndrome]], a syndrome which also includes multiple [[colon polyp]]s and osteomas. Fibromatosis is a different entity from [[neurofibromatosis]]. | Subtypes of fibromatosis include juvenile fibromatosis, fibromatosis colli, infantile digital fibromatosis, infantile myofibromatosis, lipofibromatosis, fibromatosis hyalinica multiplex, penile fibromatosis (Peyronie's disease), and palmar fibromatosis (Dupuytren's contracture). Multiple fibromatoses are seen in [[Gardner's syndrome]], a syndrome which also includes multiple [[colon polyp]]s and osteomas. Fibromatosis is a different entity from [[neurofibromatosis]]. | ||
==References== | ==References== | ||
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{{Diseases of the musculoskeletal system and connective tissue}} | {{Diseases of the musculoskeletal system and connective tissue}} | ||
{{WikiDoc Help Menu}} | {{WikiDoc Help Menu}} | ||
{{WikiDoc Sources}} | {{WikiDoc Sources}} | ||
[[Category:Disease]] | |||
[[Category:Rheumatology]] | |||
Latest revision as of 02:45, 31 October 2012
| Fibromatosis | |
| ICD-10 | M72.9 |
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| MeSH | D005350 |
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WikiDoc Resources for Fibromatosis |
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Most recent articles on Fibromatosis Most cited articles on Fibromatosis |
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Powerpoint slides on Fibromatosis |
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Evidence Based Medicine |
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Clinical Trials |
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Ongoing Trials on Fibromatosis at Clinical Trials.gov Clinical Trials on Fibromatosis at Google
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Guidelines / Policies / Govt |
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US National Guidelines Clearinghouse on Fibromatosis
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Books |
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News |
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Commentary |
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Definitions |
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Patient Resources / Community |
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Patient resources on Fibromatosis Discussion groups on Fibromatosis Patient Handouts on Fibromatosis Directions to Hospitals Treating Fibromatosis Risk calculators and risk factors for Fibromatosis
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Healthcare Provider Resources |
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Causes & Risk Factors for Fibromatosis |
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Continuing Medical Education (CME) |
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Experimental / Informatics |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Synonyms and keywords: Fibromyxoma; myxofibroma; musculoaponeurotic fibromatosis
Overview
The term fibromatosis refers to a group of benign soft tissue tumors which have certain characteristics in common, including absence of cytologic and clinical malignant features, a histology consistent with proliferation of well-differentiated fibroblasts, an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence. Other names include "musculoaponeurotic fibromatosis," referring to the tendency of these tumors to be adjacent to and infiltrating deep skeletal muscle, and "desmoid tumor," an obsolete term which more specifically refers to the occurrence of these tumors in the abdominal wall of a pregnant woman. Treatment includes prompt radical excision with a wide margin and/or radiation. Despite the local infiltrative and aggressive behavior of these tumors, mortality secondary to these tumors is minimal to nonexistent.
Classification
Subtypes of fibromatosis include juvenile fibromatosis, fibromatosis colli, infantile digital fibromatosis, infantile myofibromatosis, lipofibromatosis, fibromatosis hyalinica multiplex, penile fibromatosis (Peyronie's disease), and palmar fibromatosis (Dupuytren's contracture). Multiple fibromatoses are seen in Gardner's syndrome, a syndrome which also includes multiple colon polyps and osteomas. Fibromatosis is a different entity from neurofibromatosis.
References
Template:Diseases of the musculoskeletal system and connective tissue