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'''For patient information click [[{{PAGENAME}} (patient information)|here]]'''
{{Infobox_Disease |
{{Infobox_Disease |
   Name          = {{PAGENAME}} |
   Name          = {{PAGENAME}} |
  Image          = Interrupted aortic arch.png|
  Caption        = Hemorrhagic Necrosis; Massive, Postoperative: Gross; natural color, heart, in situ, a 2 day old infant, operative death, interrupted aortic arch and [[VSD]] <br> <small> [http://www.peir.net Image courtesy of Professor Peter Anderson DVM PhD and published with permission © PEIR, University of Alabama at Birmingham, Department of Pathology] </small>|
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   ICD10          = {{ICD10|Q|25|2|q|20}} ([[EUROCAT]]) |
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{{SI}}
{{Interrupted aortic arch}}
{{WikiDoc Cardiology Network Infobox}}
{{CMG}}


'''Associate Editor-in-Chief:''' Keri Shafer, M.D. [mailto:kshafer@bidmc.harvard.edu]
{{CMG}}; '''Associate Editor-In-Chief:''' [[Priyamvada Singh|Priyamvada Singh, M.B.B.S.]] [mailto:psingh13579@gmail.com], {{CZ}}, [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu]; '''Assistant Editor-In-Chief:''' [[Kristin Feeney|Kristin Feeney, B.S.]] [mailto:kfeeney@elon.edu]


{{Editor Join}}
==[[Interrupted aortic arch overview|Overview]]==


==Overview==
==[[Interrupted aortic arch pathophysiology|Pathophysiology]]==
'''Interrupted aortic arch''' is a very rare heart defect in which the [[aorta]] is not completely developed. There is a gap between the ascending and descending thoracic aorta. Almost all patients also have other cardiac anomalies. It can be diagnosed with an [[echocardiogram]]. Treatment consists of [[open heart surgery]] soon after birth. Awaiting surgery, [[prostaglandin]] can be administered to keep the [[ductus arteriosus]] open, thereby allowing blood flow to the lower body.


*Interrupted aortic arch (IAA) is a separation between the ascending and descending aortas. There are 3 types of this abnormality:
==[[Interrupted aortic arch epidemiology and demographics|Epidemiology and demographics]]==
:*Type A: Interruption is distal to the subclavian artery
 
:*Type B: Interruption occurs between the second carotid and the ipsilateral subclavian arteries
==[[Interrupted aortic arch natural history|Natural history, Complications, and Prognosis]]==
:*Type C: Interruption occurs between two carotid arteries.
 
*Each type is divided into 3 subtypes:
==[[Interrupted aortic arch causes|Causes]]==
:*Subtype 1: Normal subclavian artery
 
:*Subtype 2: Aberrant subclavian artery
==[[Interrupted aortic arch differential diagnosis|Differentiating Interrupted aortic arch from other Disorders]]==
:*Subtype 3: Isolated subclavian artery that arises from the ductus arteriosus.
 
*In addition to the type of IAA, the following information is important for surgical planning
==Diagnosis==
:*Evaluation of the distance between the proximal and distal segments,
[[Interrupted aortic arch history and symptoms|History and Symptoms]] | [[Interrupted aortic arch physical examination|Physical Examination]] | [[Interrupted aortic arch laboratory tests|Laboratory Tests]] | [[Interrupted aortic arch electrocardiogram | Electrocardiogram]] | [[Interrupted aortic arch chest x ray|Chest X Ray]] | [[Interrupted aortic arch MRI|MRI]] | [[Interrupted aortic arch CT|CT]] | [[Interrupted aortic arch echocardiography|Echocardiography]] | [[Interrupted aortic arch other imaging findings|Other Imaging Findings]] | [[Interrupted aortic arch other diagnostic studies|Other Diagnostic Studies]]
:*Size of a [[patent ductus arteriosus]]
 
:*Narrowest dimension of the left ventricular outflow tract
==Treatment==
:*Other cardiac structural abnormalities are important for surgical planning.
'''Medical:''' [[Interrupted aortic arch medical therapy|Medical Therapy]]
*A right-sided descending aorta with aortic interruption is almost always associated with [[DiGeorge syndrome]].
 
'''Surgical:''' [[Interrupted aortic arch surgery|Surgery]]
 
[[Interrupted aortic arch primary prevention|Primary Prevention]] | [[Interrupted aortic arch secondary prevention|Secondary Prevention]] | [[Interrupted aortic arch cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Interrupted aortic arch future or investigational therapies|Future or Investigational Therapies]]
 
==References==
{{reflist|2}}


==External links==
==External links==
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* [http://www.cincinnatichildrens.org/health/heart-encyclopedia/anomalies/iaa.htm Heart center encyclopedia]
* [http://www.cincinnatichildrens.org/health/heart-encyclopedia/anomalies/iaa.htm Heart center encyclopedia]
* [http://goldminer.arrs.org/search.php?query=Interrupted%20aortic%20arch Goldminer: Interrupted aortic arch]
* [http://goldminer.arrs.org/search.php?query=Interrupted%20aortic%20arch Goldminer: Interrupted aortic arch]
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==Additional Reading==
[[Category:Cardiovascular system]]
 
* Hyun Woo Goo, In-Sook Park, Jae Kon Ko, Yong Hwue Kim, Dong-Man Seo, Tae-Jin Yun, Jeong-Jun Park, and Chong Hyun Yoon. CT of Congenital Heart Disease: Normal Anatomy and Typical Pathologic Conditions. RadioGraphics 2003 23: S147-165S.
* Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843
 
{{Congenital malformations and deformations of circulatory system}}
{{SIB}}
[[Category:Cardiology]]
[[Category:Cardiology]]
[[Category:Congenital heart disease]]
[[Category:Congenital heart disease]]
 
[[Category:Pediatrics]]
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Latest revision as of 15:18, 2 November 2012

For patient information click here

Interrupted aortic arch
ICD-10 Q25.2 (EUROCAT)
ICD-9 747.11

Interrupted aortic arch Microchapters

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Priyamvada Singh, M.B.B.S. [2], Cafer Zorkun, M.D., Ph.D. [3], Keri Shafer, M.D. [4]; Assistant Editor-In-Chief: Kristin Feeney, B.S. [5]

Overview

Pathophysiology

Epidemiology and demographics

Natural history, Complications, and Prognosis

Causes

Differentiating Interrupted aortic arch from other Disorders

Diagnosis

History and Symptoms | Physical Examination | Laboratory Tests | Electrocardiogram | Chest X Ray | MRI | CT | Echocardiography | Other Imaging Findings | Other Diagnostic Studies

Treatment

Medical: Medical Therapy

Surgical: Surgery

Primary Prevention | Secondary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies

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