Interrupted aortic arch overview

Interrupted aortic arch Microchapters
Home
Patient Info
Overview
Pathophysiology
Epidemiology & Demographics
Risk Factors
Screening
Natural History, Complications & Prognosis
Causes of Interrupted aortic arch
Differentiating Interrupted aortic arch from other Diseases
Diagnosis
History & Symptoms
Physical Examination
Lab Tests
Electrocardiogram
Chest X Ray
MRI
CT
Echocardiography or Ultrasound
Other Imaging Findings
Other Diagnostic Studies
Treatment
Medical Therapy
Surgery
Primary Prevention
Secondary Prevention
Cost-Effectiveness of Therapy
Future or Investigational Therapies
Interrupted aortic arch overview On the Web
Most recent articles
Most cited articles
Review articles
CME Programs
Powerpoint slides
Images
American Roentgen Ray Society Images of Interrupted aortic arch overview All Images X-rays Echo & Ultrasound CT Images MRI
Ongoing Trials at Clinical Trials.gov
US National Guidelines Clearinghouse
NICE Guidance
FDA on Interrupted aortic arch overview
CDC on Interrupted aortic arch overview
Interrupted aortic arch overview in the news
Blogs on Interrupted aortic arch overview
Directions to Hospitals Treating Type page name here
Risk calculators and risk factors for Interrupted aortic arch overview

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2], Keri Shafer, M.D. [3], Priyamvada Singh, MBBS [[4]]

Assistant Editor-In-Chief: Kristin Feeney, B.S. [[5]]

Overview

Interrupted aortic arch is a very rare heart defect in which the aorta is not completely developed. There is a gap between the ascending and descending thoracic aorta. Almost all patients also have other cardiac anomalies. It can be diagnosed with an echocardiogram. Treatment consists of open heart surgery soon after birth. Awaiting surgery, prostaglandin can be administered to keep the ductus arteriosus open, thereby allowing blood flow to the lower body.

• Interrupted aortic arch (IAA) is a separation between the ascending and descending aortas. There are 3 types of this abnormality:

• Type A: Interruption is distal to the subclavian artery
• Type B: Interruption occurs between the second carotid and the ipsilateral subclavian arteries
• Type C: Interruption occurs between two carotid arteries.

• Each type is divided into 3 subtypes:

• Subtype 1: Normal subclavian artery
• Subtype 2: Aberrant subclavian artery
• Subtype 3: Isolated subclavian artery that arises from the ductus arteriosus.

• In addition to the type of IAA, the following information is important for surgical planning

• Evaluation of the distance between the proximal and distal segments,
• Size of a patent ductus arteriosus
• Narrowest dimension of the left ventricular outflow tract
• Other cardiac structural abnormalities are important for surgical planning.

• A right-sided descending aorta with aortic interruption is almost always associated with DiGeorge syndrome.

External links

• University of Michigan: Interrupted aortic arch
• Heart center encyclopedia
• Goldminer: Interrupted aortic arch