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| __NOTOC__
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| {{Congenital adrenal hyperplasia}}
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| {{CMG}}; '''Associate Editor-In-Chief:''' {{CZ}}
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| ==Overview==
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| == Epidemiology and Demographics ==
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| The incidence of congenital adrenal hyperplasia ranges from 1:10,000 to 1:20,000 births.
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| CAH is more prevalent in some ethnic groups, particularly in remote geographic regions such as Alaskan Yupiks.<ref name="pmid20823466">{{cite journal |vauthors=Speiser PW, Azziz R, Baskin LS, Ghizzoni L, Hensle TW, Merke DP, Meyer-Bahlburg HF, Miller WL, Montori VM, Oberfield SE, Ritzen M, White PC |title=Congenital adrenal hyperplasia due to steroid 21-hydroxylase deficiency: an Endocrine Society clinical practice guideline |journal=J. Clin. Endocrinol. Metab. |volume=95 |issue=9 |pages=4133–60 |year=2010 |pmid=20823466 |pmc=2936060 |doi=10.1210/jc.2009-2631 |url=}}</ref>
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| The classic type affects approximately 1 in 16,000 live births.2
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| NCCAH is one of the most common autosomal recessive disorders in humans and affects approximately 1 in 1000 individuals.3
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| The second most common form of CAH, 11b-hydroxylase deficiency (11-OHD), occurs in 1 in 100,000 live births in the general population and accounts for approximately 5% of cases.4
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| Other less common forms of CAH include 3b-hydroxysteroid dehydrogenase type 2 deficiency, 17a-hydroxylase deficiency that is more commonly seen in Brazil and Mennonite descendants from Dutch Friesland; congenital lipoid adrenal hyperplasia that is more commonly seen in the Japanese and Korean populations; side-chain cleavage (SCC) enzyme deficiency that is most commonly found in Turkey; and cytochrome P450 oxidoreductase deficiency, the only variant that can manifest with skeletal malformation
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| CAH ART
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| ==References==
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| {{Reflist|2}}
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| [[Category:Disease]]
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| [[Category:Pediatrics]]
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| [[Category:Endocrinology]]
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| [[Category:Genetic disorders]]
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| [[Category:Intersexuality]]
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