Cruveilhier-Baumgarten syndrome: Difference between revisions
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'''''Synonyms and keywords:''''' Cruveilhier-Baumgarten disease, Cruveilhier-Baumgarten bruit | |||
==Overview== | |||
A rare medical condition in which the [[Umbilical vein|umbilical]] or [[Paraumbilical vein|paraumbilical veins]] are distended. | |||
==Historical perspective== | |||
It was first described by Pégot in 1833, and then by [[Jean Cruveilhier]] (1835) and [[Paul Clemens von Baumgarten]] (1907).<ref name=gut>{{cite journal |author=Bisseru B, Patel JS |title=Cruveilhier-Baumgarten (C-B) disease |journal=Gut |volume=30 |issue=1 |pages=136–7 |year=1989 |month=January |pmid=2920918 |pmc=1378244 |doi= 10.1136/gut.30.1.136|url=http://gut.bmj.com/cgi/pmidlookup?view=long&pmid=2920918 |accessdate=2009-03-27}}</ref> | |||
Armstrong ''et al.'' (1942) and Steinburg and Galambos (1967) described two different types of the condition: Cruveilhier-Baumgarten syndrome and Cruveilhier-Baumgarten disease. | |||
==Pathophysiology== | |||
* '''Cruveilhier-Baumgarten syndrome''': liver cirrhosis or portal hypertension is the cause of the distension of the paraumbilical veins (i.e. an ''acquired'' condition in which the veins reopen due to high portal pressure). | |||
* '''Cruveilhier-Baumgarten disease''': the distension of the paraumbilical veins is due to failure of umbilical vein closure, with little or no evidence of liver disease found on liver biopsy (i.e. a ''congenital'' patency of the umbilical vein leading to portal hypertension).<ref name=gut /> | |||
==Diagnosis== | |||
===Physical examination=== | |||
* Abdominal wall [[bruit]] (the [[Cruveilhier-Baumgarten bruit]]) | |||
* Palpable thrill | |||
* [[Portal hypertension]] [[Esophageal varices|oesophageal varices]] | |||
** [[Hypersplenism]] | |||
** [[Esophageal varices|oesophageal varices]] | |||
* Normal [[liver]] | |||
==References== | |||
{{reflist|2}} | |||
{{WH}} | |||
{{WS}} | |||
[[Category:Grammar]] | |||
Latest revision as of 15:48, 27 July 2012
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Aditya Govindavarjhulla, M.B.B.S. [2] Synonyms and keywords: Cruveilhier-Baumgarten disease, Cruveilhier-Baumgarten bruit
Overview
A rare medical condition in which the umbilical or paraumbilical veins are distended.
Historical perspective
It was first described by Pégot in 1833, and then by Jean Cruveilhier (1835) and Paul Clemens von Baumgarten (1907).[1] Armstrong et al. (1942) and Steinburg and Galambos (1967) described two different types of the condition: Cruveilhier-Baumgarten syndrome and Cruveilhier-Baumgarten disease.
Pathophysiology
- Cruveilhier-Baumgarten syndrome: liver cirrhosis or portal hypertension is the cause of the distension of the paraumbilical veins (i.e. an acquired condition in which the veins reopen due to high portal pressure).
- Cruveilhier-Baumgarten disease: the distension of the paraumbilical veins is due to failure of umbilical vein closure, with little or no evidence of liver disease found on liver biopsy (i.e. a congenital patency of the umbilical vein leading to portal hypertension).[1]
Diagnosis
Physical examination
- Abdominal wall bruit (the Cruveilhier-Baumgarten bruit)
- Palpable thrill
- Portal hypertension oesophageal varices
- Normal liver
References
- ↑ 1.0 1.1 Bisseru B, Patel JS (1989). "Cruveilhier-Baumgarten (C-B) disease". Gut. 30 (1): 136–7. doi:10.1136/gut.30.1.136. PMC 1378244. PMID 2920918. Retrieved 2009-03-27. Unknown parameter
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