Ebsteins anomaly of the tricuspid valve electrocardiogram: Difference between revisions

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{{Template:Ebstein's anomaly of the tricuspid valve}}
{{Template:Ebstein's anomaly of the tricuspid valve}}


{{CMG}}; '''Associate Editor-In-Chief:''' {{CZ}}}; Claudia P. Hochberg, M.D.; [[Priyamvada Singh|Priyamvada Singh, MBBS]] [mailto:psingh@perfuse.org] '''Assistant Editor-In-Chief:''' [[Kristin Feeney|Kristin Feeney, B.S.]] [mailto:kfeeney@perfuse.org]
{{CMG}}; '''Associate Editor-In-Chief:''' {{CZ}}}; Claudia P. Hochberg, M.D.; [[Priyamvada Singh|Priyamvada Singh, MBBS]] [mailto:psingh13579@gmail.com] '''Assistant Editor-In-Chief:''' [[Kristin Feeney|Kristin Feeney, B.S.]] [mailto:kfeeney@elon.edu]


==Overview==
==Overview==
The EKG is abnormal in 50 to 60% of patients,  and will often show signs of [[right atrial enlargement]], including [["Himalayan" P waves]] which are [[P waves greater than 2.5 mm in height in leads 2, 3, and aVF]].  [[First-degree AV block]], [[low QRS voltage]], an atypical [[right bundle branch block]], [[T wave inversions]], and [[Wolff-Parkinson-White syndrome]] may also be present.
The [[EKG]] is abnormal in 50 to 60% of [[patients]],  and will often show signs of [[right atrial enlargement]], including [["Himalayan" P waves]] which are [[P waves greater than 2.5 mm in height in leads 2, 3, and aVF]].  [[First-degree AV block]], [[low QRS voltage]], an atypical [[right bundle branch block]], [[T wave inversions]], and [[Wolff-Parkinson-White syndrome]] may also be present.


==EKG Abnormalities==
==EKG Abnormalities==
* [[Right atrial enlargement]] or tall and broad [['Himalayan' P waves]]
* [[Right atrial enlargement]] or tall and broad [['Himalayan' P waves]]<ref name="pmid14387934">{{cite journal |vauthors=VAN LINGEN B, BAUERSFELD SR |title=The electrocardiogram in Ebstein's anomaly of the tricuspid valve |journal=Am. Heart J. |volume=50 |issue=1 |pages=13–23 |date=July 1955 |pmid=14387934 |doi=10.1016/0002-8703(55)90250-7 |url=}}</ref><ref name="pmid17228014">{{cite journal |vauthors=Attenhofer Jost CH, Connolly HM, Dearani JA, Edwards WD, Danielson GK |title=Ebstein's anomaly |journal=Circulation |volume=115 |issue=2 |pages=277–85 |date=January 2007 |pmid=17228014 |doi=10.1161/CIRCULATIONAHA.106.619338 |url=}}</ref>
* [[First degree atrioventricular block]] due to an [[intraatrial conduction delay]] with a [[prolonged PR-interval]]
* [[First degree atrioventricular block]] due to an [[intraatrial conduction delay]] with a [[prolonged PR-interval]]


* About 50% of individuals with Ebstein's anomaly have evidence of [[Wolff-Parkinson-White Syndrome]] (syndrome of [[pre-excitation of the ventricles]] due to an [[accessory pathway]] known as the [[Bundle of Kent]]), secondary to the the apical displacement of the septal tricuspid valve leaflet resulting in discontinuity of the central fibrous body. WPW has a left bundle branch pattern with predominant S waves in the right precordium as well as a short [[PR interval]] and a [[delta wave]].
* About 50% of individuals with Ebstein's anomaly have evidence of [[Wolff-Parkinson-White Syndrome]] (syndrome of [[pre-excitation of the ventricles]] due to an [[accessory pathway]] known as the [[Bundle of Kent]]), secondary to the the [[apical]] displacement of the septal [[tricuspid valve]] leaflet resulting in discontinuity of the central fibrous body. [[WPW]] has a [[Left bundle branch block|left bundle branch]] pattern with predominant [[S wave|S waves]] in the right [[precordium]] as well as a short [[PR interval]] and a [[delta wave]].
   
   
* [[Low amplitude QRS complexes]] in the right precordial leads,  
* [[Low amplitude QRS complexes]] in the right [[precordial leads]],


* Atypical [[right bundle branch block]]
* Atypical [[right bundle branch block]]
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* [[T wave inversion]] in V<sub>1</sub>-V<sub>4</sub> and [[Q waves]] in V<sub>1</sub>-V<sub>4</sub> and II, III and aVF.
* [[T wave inversion]] in V<sub>1</sub>-V<sub>4</sub> and [[Q waves]] in V<sub>1</sub>-V<sub>4</sub> and II, III and aVF.


* [[Supraventricular tachycardia]] and other forms of rhythm disturbances such as [[atrial flutter]] or [[atrial fibrillation]] may be observed
* [[Supraventricular tachycardia]] and other forms of [[rhythm disturbances]] such as [[atrial flutter]] or [[atrial fibrillation]] may be observed


== Electrocardiographic Example ==
== Electrocardiographic Example ==
Shown below is the EKG of a woman with '''Ebstein's anomaly'''. The ECG shows signs of [[right atrial enlargement]]. The [[P waves in leads 2,3, and aVF are tall]] and greater than 2.5 mm in height. These [[large P waves]] are termed [["Himalayan" P waves]].  There is also a [[right bundle branch block]] pattern and a [[first degree atrioventricular block]] ([[prolonged PR-interval]]) due to [[intra-atrial conduction delay]]. There is no evidence of a [[Kent-bundle]] in this patient. There is [[T wave inversion]] in V1-4 and a marked [[Q wave]] in III; these two changes are characteristic for Ebstein's anomaly and do not reflect ischemic ECG changes in this patient.
Shown below is the [[EKG]] of a woman with '''Ebstein's anomaly'''. The [[ECG]] shows signs of [[right atrial enlargement]]. The [[P waves in leads 2,3, and aVF are tall]] and greater than 2.5 mm in height. These [[large P waves]] are termed [["Himalayan" P waves]].  There is also a [[right bundle branch block]] pattern and a [[first degree atrioventricular block]] ([[prolonged PR-interval]]) due to [[intra-atrial conduction delay]]. There is no evidence of a [[Kent-bundle]] in this [[patient]]. There is [[T wave inversion]] in V1-4 and a marked [[Q wave]] in III; these two changes are characteristic for Ebstein's anomaly and do not reflect [[ischemic]] [[ECG]] changes in this [[patient]].


[[Image:Ebstein's anomaly ECG.png|center|500px]]
[[Image:Ebstein's anomaly ECG.png|center|500px]]
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Shown below is the [[electrocardiogram]] of an adolescent with Ebstein's anomaly which demonstrates [[right atrial enlargement]] and [[first-degree AV block]].  [[Right Bundle Branch Block]] and [[right axis deviation]] are also present.
[[File:Ebsteins EKG.jpg|center|500px]]
Source:  http://www.childrenshospital.org/cfapps/mml/index.cfm?CAT=media&MEDIA_ID=1623
----
----


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{{WS}}
{{WS}}


[[Category:Disease]]
[[Category:Cardiovascular system]]
[[Category:Cardiology]]
[[Category:Cardiology]]
[[Category:Congenital heart disease]]
[[Category:Pediatrics]]
[[Category:Pediatrics]]
[[Category:Disease]]

Latest revision as of 18:10, 12 February 2020

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]}; Claudia P. Hochberg, M.D.; Priyamvada Singh, MBBS [3] Assistant Editor-In-Chief: Kristin Feeney, B.S. [4]

Overview

The EKG is abnormal in 50 to 60% of patients, and will often show signs of right atrial enlargement, including "Himalayan" P waves which are P waves greater than 2.5 mm in height in leads 2, 3, and aVF. First-degree AV block, low QRS voltage, an atypical right bundle branch block, T wave inversions, and Wolff-Parkinson-White syndrome may also be present.

EKG Abnormalities

Electrocardiographic Example

Shown below is the EKG of a woman with Ebstein's anomaly. The ECG shows signs of right atrial enlargement. The P waves in leads 2,3, and aVF are tall and greater than 2.5 mm in height. These large P waves are termed "Himalayan" P waves. There is also a right bundle branch block pattern and a first degree atrioventricular block (prolonged PR-interval) due to intra-atrial conduction delay. There is no evidence of a Kent-bundle in this patient. There is T wave inversion in V1-4 and a marked Q wave in III; these two changes are characteristic for Ebstein's anomaly and do not reflect ischemic ECG changes in this patient.


Shown below is the electrocardiogram of an adolescent with Ebstein's anomaly which demonstrates right atrial enlargement and first-degree AV block. Right Bundle Branch Block and right axis deviation are also present.

Source: http://www.childrenshospital.org/cfapps/mml/index.cfm?CAT=media&MEDIA_ID=1623


References

  1. VAN LINGEN B, BAUERSFELD SR (July 1955). "The electrocardiogram in Ebstein's anomaly of the tricuspid valve". Am. Heart J. 50 (1): 13–23. doi:10.1016/0002-8703(55)90250-7. PMID 14387934.
  2. Attenhofer Jost CH, Connolly HM, Dearani JA, Edwards WD, Danielson GK (January 2007). "Ebstein's anomaly". Circulation. 115 (2): 277–85. doi:10.1161/CIRCULATIONAHA.106.619338. PMID 17228014.


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