Papuloerythroderma of Ofuji: Difference between revisions
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==Overview== | |||
Papuloerythroderma of Ofuji is a rare disorder most commonly found in Japan, characterized by pruritic [[papule]]s that spare the skinfolds, producing bands of uninvolved cutis, creating the so-called deck-chair sign. Frequently there is associated blood eosinophilia. Skin biopsies reveal a dense lymphohistiocytic infiltrate, [[eosinophils]] in the papillary dermis, and increased [[Langerhans cells]] (S-100 positive). Systemic steroids are the treatment of choice and may result in long-term remissions.<ref name="Andrews">James, William; Berger, Timothy; Elston, Dirk (2005). ''Andrews' Diseases of the Skin: Clinical Dermatology''. (10th ed.). Saunders. ISBN 0-7216-2921-0.</ref><ref name="Bolognia">{{cite book |author=Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. |title=Dermatology: 2-Volume Set |publisher=Mosby |location=St. Louis |year=2007 |pages= |isbn=1-4160-2999-0 |oclc= |doi= |accessdate=}}</ref> | |||
It was characterized in 1984.<ref name="pmid20339287">{{cite journal |author=Torchia D, Miteva M, Hu S, Cohen C, Romanelli P |title=Papuloerythroderma 2009: Two New Cases and Systematic Review of the Worldwide Literature 25 Years after Its Identification by Ofuji et al |journal=Dermatology |volume= 220|issue= 4|pages= 311–320|year=2010 |month=March |pmid=20339287 |doi=10.1159/000301915 |url=http://content.karger.com/produktedb/produkte.asp?typ=fulltext&file=000301915}}</ref><ref name="pmid6148269">{{cite journal |author=Ofuji S, Furukawa F, Miyachi Y, Ohno S |title=Papuloerythroderma |journal=Dermatologica |volume=169 |issue=3 |pages=125–30 |year=1984 |pmid=6148269 |doi= |url=}}</ref> | It was characterized in 1984.<ref name="pmid20339287">{{cite journal |author=Torchia D, Miteva M, Hu S, Cohen C, Romanelli P |title=Papuloerythroderma 2009: Two New Cases and Systematic Review of the Worldwide Literature 25 Years after Its Identification by Ofuji et al |journal=Dermatology |volume= 220|issue= 4|pages= 311–320|year=2010 |month=March |pmid=20339287 |doi=10.1159/000301915 |url=http://content.karger.com/produktedb/produkte.asp?typ=fulltext&file=000301915}}</ref><ref name="pmid6148269">{{cite journal |author=Ofuji S, Furukawa F, Miyachi Y, Ohno S |title=Papuloerythroderma |journal=Dermatologica |volume=169 |issue=3 |pages=125–30 |year=1984 |pmid=6148269 |doi= |url=}}</ref> | ||
Use of PUVA in treatment has been described.<ref name="BurgKempf2005">{{cite book|author1=Günter Burg|author2=Werner Kempf|title=Cutaneous Lymphomas|url=http://books.google.com/books?id=xtm_H3u2QYAC&pg=PA365|accessdate=30 May 2010|year=2005|publisher=Informa Health Care|isbn=978-0-8247-2997-4|pages=365–}}</ref> | Use of PUVA in treatment has been described.<ref name="BurgKempf2005">{{cite book|author1=Günter Burg|author2=Werner Kempf|title=Cutaneous Lymphomas|url=http://books.google.com/books?id=xtm_H3u2QYAC&pg=PA365|accessdate=30 May 2010|year=2005|publisher=Informa Health Care|isbn=978-0-8247-2997-4|pages=365–}}</ref> | ||
==References== | |||
{{Reflist|2}} | |||
== See also == | == See also == | ||
* [[Pruritus]] | * [[Pruritus]] | ||
* [[Erythroderma]] | * [[Erythroderma]] | ||
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Latest revision as of 17:45, 29 July 2013
Please help WikiDoc by adding content here. It's easy! Click here to learn about editing.
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Papuloerythroderma of Ofuji is a rare disorder most commonly found in Japan, characterized by pruritic papules that spare the skinfolds, producing bands of uninvolved cutis, creating the so-called deck-chair sign. Frequently there is associated blood eosinophilia. Skin biopsies reveal a dense lymphohistiocytic infiltrate, eosinophils in the papillary dermis, and increased Langerhans cells (S-100 positive). Systemic steroids are the treatment of choice and may result in long-term remissions.[1][2]
It was characterized in 1984.[3][4]
Use of PUVA in treatment has been described.[5]
References
- ↑ James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN 0-7216-2921-0.
- ↑ Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
- ↑ Torchia D, Miteva M, Hu S, Cohen C, Romanelli P (2010). "Papuloerythroderma 2009: Two New Cases and Systematic Review of the Worldwide Literature 25 Years after Its Identification by Ofuji et al". Dermatology. 220 (4): 311–320. doi:10.1159/000301915. PMID 20339287. Unknown parameter
|month=ignored (help) - ↑ Ofuji S, Furukawa F, Miyachi Y, Ohno S (1984). "Papuloerythroderma". Dermatologica. 169 (3): 125–30. PMID 6148269.
- ↑ Günter Burg; Werner Kempf (2005). Cutaneous Lymphomas. Informa Health Care. pp. 365–. ISBN 978-0-8247-2997-4. Retrieved 30 May 2010.