Angiomyolipoma epidemiology and demographics: Difference between revisions
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{{CMG}}''' Associate Editor-In-Chief:''' {{CZ}}, {{Faizan}} | {{CMG}}''' Associate Editor-In-Chief:''' {{CZ}}, {{Faizan}} | ||
Angiomyolipomas are the most common benign solid renal lesion and also the most fat containing lesion of the kidneys. The majority of angiomyolipomas are sporadic (80%) and are typically identified in adults (mean age of presentation 43 years), with a strong female predilection (F:M of 4:1) 7,9. The remaining 20% are seen in association with phakomatoses, the vast majority in the setting of tuberous sclerosis, although they have also been described in setting of Von Hippel-Lindau syndrome (VHL) and neurofibromatosis type 1 (NF1) 5,7. In these cases they present earlier (usually identified by the age of 10 years), are larger, and are far more numerous. They are more likely to be fat-poor which accounts for their earlier presentation 2,6-7. | Angiomyolipomas are the most common benign solid renal lesion and also the most fat containing lesion of the kidneys. The majority of angiomyolipomas are sporadic (80%) and are typically identified in adults (mean age of presentation 43 years), with a strong female predilection (F:M of 4:1) 7,9. The remaining 20% are seen in association with phakomatoses, the vast majority in the setting of tuberous sclerosis, although they have also been described in setting of Von Hippel-Lindau syndrome (VHL) and neurofibromatosis type 1 (NF1) 5,7. In these cases they present earlier (usually identified by the age of 10 years), are larger, and are far more numerous. They are more likely to be fat-poor which accounts for their earlier presentation 2,6-7. | ||
Revision as of 15:25, 21 September 2015
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2], Faizan Sheraz, M.D. [3]
Angiomyolipomas are the most common benign solid renal lesion and also the most fat containing lesion of the kidneys. The majority of angiomyolipomas are sporadic (80%) and are typically identified in adults (mean age of presentation 43 years), with a strong female predilection (F:M of 4:1) 7,9. The remaining 20% are seen in association with phakomatoses, the vast majority in the setting of tuberous sclerosis, although they have also been described in setting of Von Hippel-Lindau syndrome (VHL) and neurofibromatosis type 1 (NF1) 5,7. In these cases they present earlier (usually identified by the age of 10 years), are larger, and are far more numerous. They are more likely to be fat-poor which accounts for their earlier presentation 2,6-7.
Incidence
The incidence is about 0.3-3%. It occurs in more than 50% of individuals with tuberous sclerosis, often bilaterally.
Gender
Angiomyolipoma is twice as common in females as in males.