21-hydroxylase deficiency surgery: Difference between revisions
| Line 10: | Line 10: | ||
===Early-onset: Severe 21-hydroxylase deficient congenital adrenal hyperplasia=== | ===Early-onset: Severe 21-hydroxylase deficient congenital adrenal hyperplasia=== | ||
====Reconstructive surgery==== | ====Reconstructive surgery==== | ||
*[[intersex surgery|Surgery]] is not recommended for genetically male (XY) infants because the excess androgens do not produce anatomic abnormality. However, surgery for severely virilized XX infants is often performed and has become a subject of [[history of intersex surgery|debate]] in the last decade.<ref name="Wikipeadia">https://en.wikipedia.org/wiki/Congenital_adrenal_hyperplasia_due_to_21-hydroxylase_deficiency</ref> | *[[intersex surgery|Surgery]] is not recommended for genetically male (XY) infants because the excess androgens do not produce anatomic abnormality. However, surgery for severely virilized XX infants is often performed and has become a subject of [[history of intersex surgery|debate]] in the last decade.<ref name="Wikipeadia">https://en.wikipedia.org/wiki/Congenital_adrenal_hyperplasia_due_to_21-hydroxylase_deficiency URL Accessed on 10/15/2015 </ref> | ||
*Surgical reconstruction of abnormal genitalia has been offered to parents of severely [[virilization|virilized]] girls with congenital adrenal hyperplasia since the first half of the 20th century. | *Surgical reconstruction of abnormal genitalia has been offered to parents of severely [[virilization|virilized]] girls with congenital adrenal hyperplasia since the first half of the 20th century. | ||
*The purpose of surgery is: | *The purpose of surgery is: | ||
Revision as of 18:13, 15 October 2015
|
Congenital adrenal hyperplasia due to 21-hydroxylase deficiency Microchapters |
|
Differentiating Congenital adrenal hyperplasia due to 21-hydroxylase deficiency from other Diseases |
|---|
|
Diagnosis |
|
Treatment |
|
Case Studies |
|
21-hydroxylase deficiency surgery On the Web |
|
American Roentgen Ray Society Images of 21-hydroxylase deficiency surgery |
|
Directions to Hospitals Treating Congenital adrenal hyperplasia due to 21-hydroxylase deficiency |
|
Risk calculators and risk factors for 21-hydroxylase deficiency surgery |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Ahmad Al Maradni, M.D. [2]
Overview
Surgery is not the first-line treatment option for patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency. Surgical reconstruction of abnormal genitalia is usually reserved for severely virilized girls.
Surgery
Early-onset: Severe 21-hydroxylase deficient congenital adrenal hyperplasia
Reconstructive surgery
- Surgery is not recommended for genetically male (XY) infants because the excess androgens do not produce anatomic abnormality. However, surgery for severely virilized XX infants is often performed and has become a subject of debate in the last decade.[1]
- Surgical reconstruction of abnormal genitalia has been offered to parents of severely virilized girls with congenital adrenal hyperplasia since the first half of the 20th century.
- The purpose of surgery is:
- To make the external genitalia look more female than male
- To make it possible for these girls to participate in normal sexual intercourse when they grow up
- To improve chances of fertility
- To reduce the frequency of urinary infections
References
- ↑ https://en.wikipedia.org/wiki/Congenital_adrenal_hyperplasia_due_to_21-hydroxylase_deficiency URL Accessed on 10/15/2015