Hirschsprung's disease classification: Difference between revisions
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==Classification== | ==Classification== | ||
Based on the extent of colon involvement Hirschsprung's disease can be classified into the following: | Based on the extent of colon involvement Hirschsprung's disease can be classified into the following: | ||
===Rectosigmoid (short) form:=== | |||
*It is the most common form and is seen in 80 to 75% of infants diagnosed with Hirschsprung's disease. | |||
===Long segment colonic Hirschsprung disease:=== | |||
*also known as total colonic aganglionosis. | |||
*The disease has ileal involvement up to 50 cm proximal to the ileocecal junction. | |||
*It is uncommon and accounts for 5 to 7% of cases diagnosed with Hirschsprung's disease. | |||
===Ultra short segment Hirschsprung's disease:=== | |||
*Only the internal anal sphincter is affected. | |||
*It is also called as internal anal sphincter achalasia. | |||
==References== | ==References== | ||
{{WH}} | {{WH}} | ||
{{WS}} | {{WS}} | ||
Revision as of 17:50, 15 June 2017
Template:Hirschprung disease Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Ahmed Younes M.B.B.CH [2]
Overview
Classification
Based on the extent of colon involvement Hirschsprung's disease can be classified into the following:
Rectosigmoid (short) form:
- It is the most common form and is seen in 80 to 75% of infants diagnosed with Hirschsprung's disease.
Long segment colonic Hirschsprung disease:
- also known as total colonic aganglionosis.
- The disease has ileal involvement up to 50 cm proximal to the ileocecal junction.
- It is uncommon and accounts for 5 to 7% of cases diagnosed with Hirschsprung's disease.
Ultra short segment Hirschsprung's disease:
- Only the internal anal sphincter is affected.
- It is also called as internal anal sphincter achalasia.