Hirschsprung's disease classification: Difference between revisions
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==Overview== | ==Overview== | ||
Hirschsprung's disease | Hirschsprung's disease classification, based on the extent of [[Colon (anatomy)|colon]] involvement, include: rectosigmoid, long segment, and ultrashort segment disease. | ||
==Classification== | ==Classification== | ||
Hirschsprung's disease may be classified based on the extent of colon involvement into the following: | Hirschsprung's disease may be classified based on the extent of [[colon]] involvement into the following: | ||
===Rectosigmoid (short) | ===Rectosigmoid (short segment) disease:=== | ||
*It is the most common form | *It is the most common form, seen in 75-80% of infants diagnosed with Hirschsprung's disease. | ||
===Long segment | ===Long segment Hirschsprung's disease:=== | ||
*It is also known as total colonic [[aganglionosis]]. | *It is also known as total colonic [[aganglionosis]]. | ||
*The disease has [[Ileum|ileal]] involvement up to 50 cm proximal to the [[Ileocecal|ileocecal junction]]. | *The disease has [[Ileum|ileal]] involvement up to 50 cm proximal to the [[Ileocecal|ileocecal junction]]. | ||
*It is uncommon and accounts for 5 | *It is uncommon and accounts for 5-7% of cases diagnosed with Hirschsprung's disease. | ||
===Ultrashort segment Hirschsprung's disease:=== | ===Ultrashort segment Hirschsprung's disease:=== | ||
*Only the [[internal anal sphincter]] is affected. | *Only the [[internal anal sphincter]] is affected. |
Revision as of 14:58, 27 July 2017
Hirschsprung's disease Microchapters |
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Hirschsprung's disease classification On the Web |
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Ahmed Younes M.B.B.CH [2]
Overview
Hirschsprung's disease classification, based on the extent of colon involvement, include: rectosigmoid, long segment, and ultrashort segment disease.
Classification
Hirschsprung's disease may be classified based on the extent of colon involvement into the following:
Rectosigmoid (short segment) disease:
- It is the most common form, seen in 75-80% of infants diagnosed with Hirschsprung's disease.
Long segment Hirschsprung's disease:
- It is also known as total colonic aganglionosis.
- The disease has ileal involvement up to 50 cm proximal to the ileocecal junction.
- It is uncommon and accounts for 5-7% of cases diagnosed with Hirschsprung's disease.
Ultrashort segment Hirschsprung's disease:
- Only the internal anal sphincter is affected.
- It is also called as internal anal sphincter achalasia.