Pulmonary hypertension screening: Difference between revisions
Line 13: | Line 13: | ||
| style="padding: 0 5px; font-size: 100%; background: #4682B4; color: #FFFFFF; width: 40%" align=center |'''Condition''' || style="padding: 0 5px; font-size: 100%; background: #4682B4; color: #FFFFFF; width: 60%" align=center |'''Recommended screening''' | | style="padding: 0 5px; font-size: 100%; background: #4682B4; color: #FFFFFF; width: 40%" align=center |'''Condition''' || style="padding: 0 5px; font-size: 100%; background: #4682B4; color: #FFFFFF; width: 60%" align=center |'''Recommended screening''' | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |''' Known [[BMPR2]] [[mutation]]''' || style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Echocardiogram]] (yearly) | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''BMPR2 [[mutation]] in a first degree relative''' || style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Genetic counseling]] <br> [[BMPR2]] genotyping | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''Family history for PAH in 2 or more relatives'''||style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left | [[Genetic counseling]] <br> [[BMPR2]] genotyping | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''[[Systemic sclerosis]]'''|| style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Echocardiogram]] (yearly) | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''[[Portal hypertension]]''' || style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Echocardiogram]] if orthotopic liver transplantation is in consideration | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''[[Sickle cell disease]]''' || style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Echocardiogram]] (yearly) | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''Previous use of [[fenfluramine]]''' || style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Echocardiogram]] in case of symptoms | ||
|- | |- | ||
|style="font-size: 100; padding: 0 5px; background: # | |style="font-size: 100; padding: 0 5px; background: #DCDCDC" align=left |'''[[Congenital heart disease]]''' || style="font-size: 100; padding: 0 5px; background: #F5F5F5" align=left |[[Echocardiogram]] at the time of diagnosis | ||
|} | |} | ||
Revision as of 18:15, 26 March 2018
Pulmonary Hypertension Microchapters |
Diagnosis |
---|
Treatment |
Case Studies |
Pulmonary hypertension screening On the Web |
American Roentgen Ray Society Images of Pulmonary hypertension screening |
Risk calculators and risk factors for Pulmonary hypertension screening |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Assistant Editor(s)-in-Chief: Ralph Matar
Overview
Patients with a known BMPR2 mutation, scleroderma, and portal hypertension undergoing evaluation for liver transplantation should receive periodic screening for pulmonary hypertension (PH) through a thorough assessment of the presence of symptoms, physical examination, chest X ray, electrocardiography, and echocardiogram. Additional investigation with right heart catheterization should be performed if screening is suggestive of the presence of PH.[1]
Screening
Shown below is a table summarizing the recommended screening in several medical conditionas associated with elevated risk for PH.[2]
Condition | Recommended screening |
Known BMPR2 mutation | Echocardiogram (yearly) |
BMPR2 mutation in a first degree relative | Genetic counseling BMPR2 genotyping |
Family history for PAH in 2 or more relatives | Genetic counseling BMPR2 genotyping |
Systemic sclerosis | Echocardiogram (yearly) |
Portal hypertension | Echocardiogram if orthotopic liver transplantation is in consideration |
Sickle cell disease | Echocardiogram (yearly) |
Previous use of fenfluramine | Echocardiogram in case of symptoms |
Congenital heart disease | Echocardiogram at the time of diagnosis |
Echocardiography findings that are suggestive of PH include:[3]
- Enlargement of the size of right atrium and right ventricle
- Decrease in the function of the right ventricle
- Displacement of the interventricular septum
- Tricuspid regurgitation
- Presence of pericardial effusion