Eisenmenger’s syndrome classification: Difference between revisions
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==Classification== | ==Classification== | ||
Diller et al. classified patients with [[Eisenmenger's syndrome]] according to the underlying [[congenital heart disease]] into<ref name="pmid17325254">{{cite journal| author=Diller GP, Gatzoulis MA| title=Pulmonary vascular disease in adults with congenital heart disease. | journal=Circulation | year= 2007 | volume= 115 | issue= 8 | pages= 1039-50 | pmid=17325254 | doi=10.1161/CIRCULATIONAHA.105.592386 | pmc= | url=https://www.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pubmed&tool=sumsearch.org/cite&retmode=ref&cmd=prlinks&id=17325254 }}</ref>: | * Diller et al. classified patients with [[Eisenmenger's syndrome]] according to the underlying [[congenital heart disease]] into<ref name="pmid17325254">{{cite journal| author=Diller GP, Gatzoulis MA| title=Pulmonary vascular disease in adults with congenital heart disease. | journal=Circulation | year= 2007 | volume= 115 | issue= 8 | pages= 1039-50 | pmid=17325254 | doi=10.1161/CIRCULATIONAHA.105.592386 | pmc= | url=https://www.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pubmed&tool=sumsearch.org/cite&retmode=ref&cmd=prlinks&id=17325254 }}</ref>: | ||
*Simple: [[Atrial septal defect|ASD]], [[Ventricular septal defect|VSD]], persistent [[ductus arteriosus]], and [[aortopulmonary window]]. | **Simple: [[Atrial septal defect|ASD]], [[Ventricular septal defect|VSD]], persistent [[ductus arteriosus]], and [[aortopulmonary window]]. | ||
*Complex: [[Pulmonary atresia]] with [[Ventricular septal defect|VSD]], [[tricuspid atresia]], [[atrioventricular septal defect]], and [[tetralogy of Fallot]]. | **Complex: [[Pulmonary atresia]] with [[Ventricular septal defect|VSD]], [[tricuspid atresia]], [[atrioventricular septal defect]], and [[tetralogy of Fallot]]. | ||
According to the histopathologic criteria of Heath and Edwards, there are six stages of pulmonary vascular disease (including [[Eisenmenger's syndrome]]): | |||
** Stage I: Medial [[Hypertrophy (medical)|hypertrophy]] (reversible) | |||
** Stage II: Cellular intimal [[hyperplasia]] in an abnormally muscular artery (reversible) | |||
** Stage III: Lumen [[occlusion]] from intimal [[hyperplasia]] of fibroelastic tissue (partially reversible) | |||
** Stage IV: Arteriolar dilatation and medial thinning (irreversible) | |||
** Stage V: Plexiform lesion, which is an angiomatoid formation (terminal and irreversible) | |||
** Stage VI: Fibrinoid/necrotizing [[arteritis]] (terminal and irreversible) | |||
==References== | ==References== | ||
{{Reflist|2}} | {{Reflist|2}} |
Revision as of 14:50, 26 January 2020
Eisenmenger’s syndrome Microchapters |
Diagnosis |
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Eisenmenger’s syndrome ACC/AHA Guidelines for Evaluation of Patients |
Treatment |
Eisenmenger’s syndrome classification On the Web |
American Roentgen Ray Society Images of Eisenmenger’s syndrome classification |
Risk calculators and risk factors for Eisenmenger’s syndrome classification |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Abdelrahman Ibrahim Abushouk, MD[2]
Overview
[Disease name] may be classified according to [classification method] into [number] subtypes/groups: [group1], [group2], [group3], and [group4].
Classification
- Diller et al. classified patients with Eisenmenger's syndrome according to the underlying congenital heart disease into[1]:
- Simple: ASD, VSD, persistent ductus arteriosus, and aortopulmonary window.
- Complex: Pulmonary atresia with VSD, tricuspid atresia, atrioventricular septal defect, and tetralogy of Fallot.
According to the histopathologic criteria of Heath and Edwards, there are six stages of pulmonary vascular disease (including Eisenmenger's syndrome):
- Stage I: Medial hypertrophy (reversible)
- Stage II: Cellular intimal hyperplasia in an abnormally muscular artery (reversible)
- Stage III: Lumen occlusion from intimal hyperplasia of fibroelastic tissue (partially reversible)
- Stage IV: Arteriolar dilatation and medial thinning (irreversible)
- Stage V: Plexiform lesion, which is an angiomatoid formation (terminal and irreversible)
- Stage VI: Fibrinoid/necrotizing arteritis (terminal and irreversible)
References
- ↑ Diller GP, Gatzoulis MA (2007). "Pulmonary vascular disease in adults with congenital heart disease". Circulation. 115 (8): 1039–50. doi:10.1161/CIRCULATIONAHA.105.592386. PMID 17325254.