Tricuspid atresia natural history, complications and prognosis: Difference between revisions
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* Complications of [[Fontan procedure]] include: | * Complications of [[Fontan procedure]] include: | ||
*[[Exercise intolerance]] due to [[ventricular failure]] | |||
*[[Pericardial effusion]] and[[ pleural effusion]], [[chylothorax]] and [[protein-losing enteropathy]] due to [[lymphatic dysfunction]] | |||
*[[Pulmonary embolism]], blood clot formation in shunt | |||
*[[Liver failure]] and portal hypertension as a result of increased pressure in the shunt | |||
*[[leakage]] of the[[ anastomosis]] | |||
*[[Pulmonary hypertension]] | |||
*[[Right atrium]] dilation | |||
*[[Arrhythmia]] | |||
==Natural History, Complications, and Prognosis== | ==Natural History, Complications, and Prognosis== | ||
Revision as of 14:32, 24 August 2020
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor-In-Chief:Sara Zand, M.D.[2] Keri Shafer, M.D. [3] Priyamvada Singh, MBBS [4] Assistant Editor-In-Chief: Kristin Feeney, B.S. [5]
Natural History, Complications and Prognosis
- Early clinical features in infants include cyanosis of lips and tongue, difficulty in breathing, tiring easily during feeding.
- The severity of cyanosis ininfants with pulmonary stenosis is dependent on the amount ofpulmonary blood flow passing throughpatent ductus arteriosus.
- After physiologic closure of patent ductus arteriosus (PDA), thecyanosis will be aggravated.
- In patients with normal pulmonary blood flow, complications ofheart failure may occur.
- Prognosis is generally poor without surgery and 90% of patients will die before 10 years old.
- The 15-year survival of patients with Fontan procedure is approximately %92 according to Merry et al.
- Complications of Fontan procedure include:
- Exercise intolerance due to ventricular failure
- Pericardial effusion andpleural effusion, chylothorax and protein-losing enteropathy due to lymphatic dysfunction
- Pulmonary embolism, blood clot formation in shunt
- Liver failure and portal hypertension as a result of increased pressure in the shunt
- leakage of theanastomosis
- Pulmonary hypertension
- Right atrium dilation
- Arrhythmia
Natural History, Complications, and Prognosis
Natural History
Complications
- Irregular, fast heart rhythms (arrhythmias)
- Chronic diarrhea (from a disease called protein losing enteropathy)
- Heart failure
- Fluid in the abdomen (ascites) and in the lungs (pleural effusion)
- Blockage of the artificial shunt
- Strokes and other neurological complications
- Sudden death
Prognosis
- The prognosis is poor in untreated patients.[1]
References
- ↑ Rao PS (2000). "Tricuspid Atresia". Curr Treat Options Cardiovasc Med. 2 (6): 507–520. doi:10.1007/s11936-000-0046-6. PMID 11096554.