Angiomyolipoma: Difference between revisions
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==Overview== | ==Overview== | ||
'''Angiomyolipoma''' is a benign [[kidney|renal]] lesion. | '''Angiomyolipoma''' is a benign [[kidney|renal]] lesion. It is a choristoma composed of variable amounts of [[fat]], [[Blood vessel|vascular]], and [[smooth muscle]] elements. The lesion is well demarcated and contains mature elements. The incidence is about 0.3-3%. It occurs in more than 50% of individuals with [[tuberous sclerosis]], often bilaterally. | ||
It is twice as common in females as in males. The fat density of the tumour on [[CT]] is [[pathognomonic]]. | |||
==Types== | |||
* Isolated Angiomyolipoma (80%) | |||
** Angiomyolipoma is about 4 times more common in women than in men. | |||
** Interestingly, 80% of the cases involve the right kidney. | |||
* Angiomyolipoma associated with [[tuberous sclerosis]] (20%). | |||
** Angiomyolipoma occurs in 80% patients with tuberous sclerosis. | |||
** Angiomyolipoma also occurs young women with [[lymphangiomyomatosis]] without other stigmata of tuberous sclerosis. AML and lymphangiomyomatosis are sometimes considered the forme fruste of tuberous sclerosis. | |||
==Diagnosis== | |||
* Most small lesions are asymptomatic and incidental findings on images. | |||
* Complications include hematuria, flank pain, and shock as a result of spontaneous hemorrhage. | |||
==Diagnostic Findings== | ==Diagnostic Findings== | ||
Revision as of 17:12, 7 March 2009
| Angiomyolipoma | |
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| ICD-10 | D30.0 |
| ICD-9 | 223.0 |
| ICD-O: | M8860/0 |
| DiseasesDB | 29496 |
| MeSH | D018207 |
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Overview
Angiomyolipoma is a benign renal lesion. It is a choristoma composed of variable amounts of fat, vascular, and smooth muscle elements. The lesion is well demarcated and contains mature elements. The incidence is about 0.3-3%. It occurs in more than 50% of individuals with tuberous sclerosis, often bilaterally.
It is twice as common in females as in males. The fat density of the tumour on CT is pathognomonic.
Types
- Isolated Angiomyolipoma (80%)
- Angiomyolipoma is about 4 times more common in women than in men.
- Interestingly, 80% of the cases involve the right kidney.
- Angiomyolipoma associated with tuberous sclerosis (20%).
- Angiomyolipoma occurs in 80% patients with tuberous sclerosis.
- Angiomyolipoma also occurs young women with lymphangiomyomatosis without other stigmata of tuberous sclerosis. AML and lymphangiomyomatosis are sometimes considered the forme fruste of tuberous sclerosis.
Diagnosis
- Most small lesions are asymptomatic and incidental findings on images.
- Complications include hematuria, flank pain, and shock as a result of spontaneous hemorrhage.
Diagnostic Findings
MRI, CT, and US images demonstrate an angiomyolipoma
Large right angiomyolipoma
