Noncompaction cardiomyopathy epidemiology and demographics: Difference between revisions
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This is a rare genetic disorder. The incidence may increase as imaging modalities improve. | This is a rare genetic disorder. The incidence may increase as imaging modalities improve. | ||
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The incidence is estimated to be 0.12 cases per 100,000 children <ref>Botto, LD. Left ventricular noncompaction. Orphanet encyclopedia. http://www.orpha.net/data/patho/GB/uk-LVNC.pdf </ref>. | The incidence is estimated to be 0.12 cases per 100,000 children <ref>Botto, LD. Left ventricular noncompaction. Orphanet encyclopedia. http://www.orpha.net/data/patho/GB/uk-LVNC.pdf </ref>. | ||
Revision as of 19:00, 6 August 2011
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
This is a rare genetic disorder. The incidence may increase as imaging modalities improve.
Prevalence in Children
The incidence is estimated to be 0.12 cases per 100,000 children [1].
Incidence in Infants
Others have estimated the rate to be as high as 0.81 per 100,000 infants per calender year.
Male Predominance
There is an excess incidence of the disease in males (56% to 82%). This has been taken as evidence that in some cases there may be x-linked inheritance.
Age
In the initial description of the disease, the median age at diagnosis was 7 with a range from 11 months to 22 years[2]. Other studies have confirmed the presence of NCC in all age groups including the elderly.
References
- ↑ Botto, LD. Left ventricular noncompaction. Orphanet encyclopedia. http://www.orpha.net/data/patho/GB/uk-LVNC.pdf
- ↑ Chin TK, Perloff JK, Williams RG, et al. Isolated noncompaction of left ventricular myocardium: a study of eight cases. Circulation. 1990; 82: 507–513.