Hemangioendothelioma: Difference between revisions

Jump to navigation Jump to search
Vanbot (talk | contribs)
m Robot: Changing Category:Diseases to Category:Disease
Lakshmi Gopalakrishnan (talk | contribs)
No edit summary
Line 1: Line 1:
'''For patient information, click [[Hemangioendothelioma (patient information)|here]]'''
{{DiseaseDisorder infobox |
{{DiseaseDisorder infobox |
   Name        = Hemangioendothelioma |
   Name        = Hemangioendothelioma |
Line 5: Line 7:
   ICDO        = 9130-9133 |
   ICDO        = 9130-9133 |
}}
}}
{{SI}}
{{Hemangioendothelioma}}
{{CMG}}
{{CMG}}
__NOTOC__
{{Editor Help}}


==Overview==
==[[Hemangioendothelioma overview|Overview]]==


'''Hemangioendothelioma''' is used to describe a group of vascular neoplasms that may be considered [[benign]] or [[malignant]] in their activity. They have been described as masses that fall between a [[hemangioma]] and [[angiosarcoma]]. They are [[vascular tumor]]s that commonly present with an enlarging mass and have been reported in the [[head]] and [[neck]], [[intestines]], [[lungs]], [[lymph nodes]], [[pleura]], [[retroperitoneum]], [[stomach]], and many other body sites. Surgical [[resection]], [[radiotherapy]], and [[chemotherapy]] have all been used to treat these masses.
==[[Hemangioendothelioma classification|Classification]]==


In hemangioendotheliomas, the cell of origin is the endothelial cell, and they range from benign to frankly malignant lesions.
==[[Hemangioendothelioma historical perspective|Historical Perspective]]==


They typically occur in young patients, especially in the soft tissues of the limbs and are often closely related to veins, from which they are thought to arise. Less frequently they can arise in bone (osseous haemangioendothelioma), in which case they are most often seen in the calvaria, spine or lower limbs.
==[[Hemangioendothelioma pathophysiology|Pathophysiology]]==


== Types of Hemangioendotheliomas ==
==[[Hemangioendothelioma epidemiology and demographics|Epidemiology & Demographics]]==
*Epithelioid
*Kaposiform
*Retiform
*[[Infantile hemangioendothelioma]]


==Diagnosis==
==[[Hemangioendothelioma epidemiology and demographics|Risk Factors]]==


Radiologically they appear the same as angiosarcomas and haemangiopericytomas.
==[[Hemangioendothelioma screening|Screening]]==


===X-rays===
==[[Hemangioendothelioma causes|Causes]]==


Nonspecific soft tissue mass. When involving bone, they are predominatly lytic, and may mimic haemangiomas with a course honeycomb appearance.
==[[Hemangioendothelioma differential diagnosis|Differentiating Hemangioendothelioma from other Diseases]]==


===Angiography===
==[[Hemangioendothelioma natural history|Natural History, Complications & Prognosis]]==


Dense, well-circumscribed areas of enhancement with early draining veins and shunting. Hemangiopericytoma are described as having a pedicle formed by the arteries supplying the tumor from which vessels branch to encircle the tumor.
==Diagnosis==
 
[[Hemangioendothelioma history and symptoms|History & Symptoms]] | [[Hemangioendothelioma physical examination|Physical Examination]] | [[Hemangioendothelioma staging|Staging]] | [[Hemangioendothelioma laboratory tests|Lab Tests]] | [[Hemangioendothelioma electrocardiogram|Electrocardiogram]] | [[Hemangioendothelioma x ray|X Ray]] | [[Hemangioendothelioma CT|CT]] | [[Hemangioendothelioma MRI|MRI]] | [[Hemangioendothelioma echocardiography or ultrasound|Echocardiography or Ultrasound]] | [[Hemangioendothelioma other imaging findings#Angiography|Angiography]] | [[Hemangioendothelioma other diagnostic studies|Other Diagnostic Studies]]
===CT===


Non specific soft tissue mass, with density similar to muscle but demonstrating bright contrast enhancement. CTA may demonstrate large feeding vessels.
==Treatment==
[[Hemangioendothelioma medical therapy|Medical Therapy]] | [[Hemangioendothelioma surgery|Surgery]] | [[Hemangioendothelioma primary prevention|Primary Prevention]] | [[Hemangioendothelioma secondary prevention|Secondary Prevention]]


===MRI===
==Resources==
 
Brightly enhancing soft tissue mass, often hyperintense on T2WI, with prominant flow voids, most marked in hemangiopericytomas.
 
==References==
 
* Murphy M. et al "Musculoskeletal Angiomatous Lesions" RadioGraphics: July 1, 1995 -- Volume 15, Number 4
 
==External links==
* [http://survivor-support.rare-cancer.org/forum/ Hemgioendothelioma Support Group]
* [http://survivor-support.rare-cancer.org/forum/ Hemgioendothelioma Support Group]
* [http://www.maxillofacialcenter.com/BondBook/softtissue/hemangioendoth.html Maxillofacialcenter]
* [http://www.maxillofacialcenter.com/BondBook/softtissue/hemangioendoth.html Maxillofacialcenter]
* [http://www.HEARDsupport.org/ '''H.E.A.R.D.''' '''H'''emangioendothelioma, '''E'''pithelioid Hemangioendothelioma '''A'''nd '''R'''elated vascular '''D'''isorders Support Group and International H.E.A.R.D. Registry]
* [http://www.HEARDsupport.org/ '''H.E.A.R.D.''' '''H'''emangioendothelioma, '''E'''pithelioid Hemangioendothelioma '''A'''nd '''R'''elated vascular '''D'''isorders Support Group and International H.E.A.R.D. Registry]


{{Soft tissue tumors and sarcomas}}


{{Soft tissue tumors and sarcomas}}
{{SIB}}
{{WikiDoc Help Menu}}
{{WikiDoc Help Menu}}
{{WikiDoc Sources}}
{{WikiDoc Sources}}


[[Category:Disease]]
[[Category:Disease]]
[[Category:Types of cancer]]
[[Category:Oncology]]
[[Category:Oncology]]

Revision as of 18:08, 21 January 2012

For patient information, click here

Template:DiseaseDisorder infobox Template:Hemangioendothelioma Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Classification

Historical Perspective

Pathophysiology

Epidemiology & Demographics

Risk Factors

Screening

Causes

Differentiating Hemangioendothelioma from other Diseases

Natural History, Complications & Prognosis

Diagnosis

History & Symptoms | Physical Examination | Staging | Lab Tests | Electrocardiogram | X Ray | CT | MRI | Echocardiography or Ultrasound | Angiography | Other Diagnostic Studies

Treatment

Medical Therapy | Surgery | Primary Prevention | Secondary Prevention

Resources


Template:WikiDoc Sources