Lymphangiomyomatosis: Difference between revisions

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==Characteristic Features==
==Characteristic Features==
Lymphangiomyocytosis is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels.  
Lymphangiomyocytosis is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels.


==Sites of Involvement==
==Sites of Involvement==

Revision as of 17:48, 14 September 2012

Template:Lymphangiomyomatosis Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-In-Chief: Varun Kumar, M.B.B.S. [2]

Synonyms and keywords: Lymphangioleiomyomatosis; LAM

Overview

Lymphangiomyocytosis is defined as a multifocal neoplasm with differentiation of the perivascular epithelioid cell and has a female prepondrance, especially females of child-bearing age.

Characteristic Features

Lymphangiomyocytosis is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels.

Sites of Involvement

  • Lungs,
  • Mediastinum, and
  • Retroperitoneum.

Presentation

It usually presents with chylous pleural effusion or ascites.

Diagnosis

Chest X-ray

Reference

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