Lung agenesis: Difference between revisions
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==Epidemiology and Demographics== | ==Epidemiology and Demographics== | ||
Lung agenesis is extremely rare. | Lung agenesis is extremely rare and is observed in 1:15,000 autopsies. | ||
===Gender=== | |||
There is a slight female preponderance. | |||
==Natural History, Complications, Prognosis== | ==Natural History, Complications, Prognosis== | ||
Revision as of 14:12, 16 September 2012
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Lung agenesis is defined as partial or complete failure of the lung to form with absence of the lung parenchyma, the bronchus and the pulmonary vessels.
Classification
The condition can be unilateral (compatible with life) or bilateral (fatal).
Pathophysiology
On the affected side, the pleural cavity is absent, and the healthy lung occupies the entire thorax.
Associated Conditions
Epidemiology and Demographics
Lung agenesis is extremely rare and is observed in 1:15,000 autopsies.
Gender
There is a slight female preponderance.
Natural History, Complications, Prognosis
Natural History
The natural history is variable.
Complications
There can be kinking of the trachea and compression of the trachea.
Prognosis
Although 50% of patients may die before the age of 5, the remainder of the individuals may be asymptomatic throughout their lives. Bilateral lung agenesis is a lethal anomaly.
References
- ↑ Krivchenya DU, Dubrovin AG, Krivchenya TD, Khursin VN, Lysak CV (2000). "Aplasia of the right lung in a 4-year-old child: surgical stabilization of the mediastinum by diaphragm translocation leading to complete recovery from respiratory distress syndrome". Journal of Pediatric Surgery. 35 (10): 1499–502. doi:10.1053/jpsu.2000.16424. PMID 11051161. Retrieved 2012-09-16. Unknown parameter
|month=ignored (help) - ↑ Skandalakis JE, Gray SW, Symbas P: The trachea and the lungs. In: Skandalakis JE, Gray SW, editors. Embryology for Surgeons. 2nd ed. Baltimore, MD: Williams and Wilkins; 1994. p 429-32.