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| ==Incidence==
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| It is believed that around one in every 1200 Americans has a Primary Immunodeficiency disorder.
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| Conditions - there are over 130 recognised primary immunodeficiencies - common variable immunodeficiency, IgA deficiency, XLA, XLP all being worthy of mention in addition to those listed.
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| Patient support - there are a growing number of national patient organisations around the world to support those who are diagnosed or where one of the conditions are recorded in a family. Access via www.ipopi.org or e-mail info@ipopi.org [or] The Immune Deficiency Foundation [or] Jeffrey Modell Foundation (Links found under "External Links Section")
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| ==Treatment==
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| Primary immunodeficiency is generally treated by [[immunotherapy]] either through intravenous infusions of [[immunoglobulin]] ([[IVIG]]) in an effort to induce [[passive immunity]] (Immunotherapy is not indicated for those who are IgA deficient). A new subcutaneous treatment (SC-Ig) was recently approved by the FDA, which is especially recommended in cases of severe adverse effects to the IV-Ig treatment or with individuals with poor venous access. Persons with immunodeficiencies are very vulnerable to [[opportunistic infection]]s, and the use of [[antimicrobial]] agents, such as [[antibiotic]]s and [[antifungal]]s, is often required. One of the future prospects in the treatment primary immunodeficiency is [[gene therapy]]. However, this form of treatment is in its infancy, and the feasibility and long-term complications of gene therapy are not known.
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| Along with physical treatment, there are hotlines and patient groups; this enables support for family members as well as the actual patient. One can find a diversity of supports by clicking the link to the 'Immune Deficiency Foundation' or 'Jeffrey Modell Foundation'' under Wikipedia's section ''External Links'' on this page.
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| ==External links==
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| Immune Deficiency Foundation [http://www.primaryimmune.org]
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| Primary Immunodeficiency Resource Center Presented by the Jeffrey Modell Foundation [http://www.info4pi.org/index.cfm?CFID=11982666&CFTOKEN=43062451.com Jeffrey Modell Foundation]
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| [[Category:Immune system disorders]]
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| International Patient Organisation for Primary Immunodeficiencies (IPOPI) [http://www.ipopi.org]
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| Population Prevalence of Diagnosed Primary Immunodeficiency Diseases in the United States [http://www.springerlink.com/content/b5r702t2820mk6l8/fulltext.pdf]
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| {{Immune_system}} | | {{Immune_system}} |