Right ventricular outflow tract obstruction pulmonary supravalvular stenosis: Difference between revisions
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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''1.'''Patients with suspected supravalvular, branch, or peripheral PS should have baseline imaging with echocardiography- Doppler plus 1 of the following: MRI angiography, CT angiography, or contrast angiography.''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])'' <nowiki>"</nowiki> | | bgcolor="LightGreen"|<nowiki>"</nowiki>'''1.'''Patients with suspected supravalvular, branch, or peripheral PS should have baseline imaging with echocardiography- Doppler plus 1 of the following: MRI angiography, CT angiography, or contrast angiography.''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])'' <nowiki>"</nowiki> | ||
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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''2.'''Once the diagnosis is established, follow-up echocardiography- Doppler to assess RV systolic pressure should be performed periodically, depending on severity.''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])'' <nowiki>"</nowiki> | |||
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==Treatment== | |||
===Surgery and Device based Therapy=== | |||
====ACC / AHA Guidelines - Recommendations for interventional therapy in the management of branch and peripheral Pulmonary Stenosis (DO NOT EDIT)==== | |||
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| colspan="1" style="text-align:center; background:LightGreen"|[[ACC AHA guidelines classification scheme#Classification of Recommendations|Class I]] | |||
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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''1.'''Percutaneous interventional therapy is recommended as the treatment of choice in the management of appropriate focal branch and/or peripheral pulmonary artery stenosis with greater than 50% diameter narrowing, an elevated RV systolic pressure greater than 50 mm Hg, and/or symptoms.''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])'' <nowiki>"</nowiki> | |||
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| bgcolor="LightGreen"|<nowiki>"</nowiki>'''2.'''Once the diagnosis is established, follow-up echocardiography- Doppler to assess RV systolic pressure should be performed periodically, depending on severity.''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])'' <nowiki>"</nowiki> | | bgcolor="LightGreen"|<nowiki>"</nowiki>'''2.'''Once the diagnosis is established, follow-up echocardiography- Doppler to assess RV systolic pressure should be performed periodically, depending on severity.''([[ACC AHA guidelines classification scheme#Level of Evidence|Level of Evidence: C]])'' <nowiki>"</nowiki> | ||
Revision as of 15:00, 5 October 2012
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Right ventricular outflow tract obstruction Microchapters |
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Classification |
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Differentiating Right ventricular outflow tract obstruction from other Diseases |
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Diagnosis |
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Treatment |
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Special Scenarios |
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Case Studies |
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Right ventricular outflow tract obstruction pulmonary supravalvular stenosis On the Web |
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FDA on Right ventricular outflow tract obstruction pulmonary supravalvular stenosis |
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CDC on Right ventricular outflow tract obstruction pulmonary supravalvular stenosis |
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Right ventricular outflow tract obstruction pulmonary supravalvular stenosis in the news |
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Blogs on Right ventricular outflow tract obstruction pulmonary supravalvular stenosis |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]; Associate Editor-in-Chief: Keri Shafer, M.D. [3]
Overview
Supra valvular pulmonary artery stenosis is defined as stenosis of the pulmonary artery above the level of the valve area.
Anatomy
1. Also called peripheral pulmonary stenosis.
2. May have one or many stenoses of the PA or its branches.
3. Infrequently occurs as an isolated lesion, more commonly occurs as part of Tetralogy of Fallot.
Diagnosis
Physical Examination
1. The murmur is most prominent at the upper left sternal border, axillae, and the posterior lung fields.
Imaging
Echocardiography
ACC / AHA Guidelines - Recommendations for evaluation of patients with supravalvular, branch, and peripheral Pulmonary Stenosis (DO NOT EDIT)
| Class I |
| "1.Patients with suspected supravalvular, branch, or peripheral PS should have baseline imaging with echocardiography- Doppler plus 1 of the following: MRI angiography, CT angiography, or contrast angiography.(Level of Evidence: C) " |
| "2.Once the diagnosis is established, follow-up echocardiography- Doppler to assess RV systolic pressure should be performed periodically, depending on severity.(Level of Evidence: C) " |
Treatment
Surgery and Device based Therapy
ACC / AHA Guidelines - Recommendations for interventional therapy in the management of branch and peripheral Pulmonary Stenosis (DO NOT EDIT)
| Class I |
| "1.Percutaneous interventional therapy is recommended as the treatment of choice in the management of appropriate focal branch and/or peripheral pulmonary artery stenosis with greater than 50% diameter narrowing, an elevated RV systolic pressure greater than 50 mm Hg, and/or symptoms.(Level of Evidence: C) " |
| "2.Once the diagnosis is established, follow-up echocardiography- Doppler to assess RV systolic pressure should be performed periodically, depending on severity.(Level of Evidence: C) " |