Ebsteins anomaly of the tricuspid valve pathophysiology

Ebsteins anomaly of the tricuspid valve Microchapters
Home
Patient Information
Overview
Historical Perpective
Classification
Pathophysiology
Causes
Differentiating Ebstein's Anomaly from other Diseases
Epidemiology and Demographics
Risk Factors
Screening
Natural History, Complications and Prognosis
Diagnosis
Diagnostic Study of Choice
History and Symptoms
Physical Examination
Laboratory Findings
Electrocardiogram
X Ray
Echocardiography
CT
MRI
Other Imaging Findings
Other diagnostic studies
Treatment
Medical Therapy
Surgery
Primary Prevention
Secondary Prevention
Case Studies
Case #1
Ebsteins anomaly of the tricuspid valve pathophysiology On the Web
Most recent articles
Most cited articles
Review articles
CME Programs
Powerpoint slides
Images
American Roentgen Ray Society Images of Ebsteins anomaly of the tricuspid valve pathophysiology All Images X-rays Echo & Ultrasound CT Images MRI
Ongoing Trials at Clinical Trials.gov
US National Guidelines Clearinghouse
NICE Guidance
FDA on Ebsteins anomaly of the tricuspid valve pathophysiology
CDC on Ebsteins anomaly of the tricuspid valve pathophysiology
Ebsteins anomaly of the tricuspid valve pathophysiology in the news
Blogs on Ebsteins anomaly of the tricuspid valve pathophysiology
Directions to Hospitals Treating Type page name here
Risk calculators and risk factors for Ebsteins anomaly of the tricuspid valve pathophysiology

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] and Claudia P. Hochberg, M.D. [2]

Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [3]}; Priyamvada Singh, MBBS [[4]] Assistant Editor-In-Chief: Kristin Feeney, B.S. [[5]]

Overview

The pathophysiology of Ebstein's anomaly depends on the morphology of tricuspid valve and right ventricle.

Tricuspid valve

• The anterior leaflet of the tricuspid valve is malformed in this condition i.e. they are attached to tricuspid valve annulus or to the right ventricular endocardium
• The septal and posterior leaflets are absent most of the times.
• Due to these changes the tricuspid valve may becomes funnel-shaped and incompetent.

Right ventricle

The right ventricular changes are secondary to the malformed tricuspid valves. The right ventricle can thus be divided into two parts by the valve

• The downward extension of the tricuspid valve causes 'atrialization' of the proximal part of the right ventricle
• The small distal part, the right ventricle proper, thus is reduced in size and sometimes comprises only of the right outflow tract.

Associated Conditions

• 50% of patients have ASD or patent foramen ovale
• 25% have accesory pathway