Lutembacher's syndrome: Difference between revisions

Revision as of 21:07, 6 August 2013

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Lutembacher's syndromeis a rare form of congenital heart disease. It refers to a combination of congenital atrial septal defect complicated by an acquired mitral stenosis.

This is a very rare disease. The incidence is 0.001/1000000^[1].

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 ==Overview==
 '''Lutembacher's syndrome'''is a rare form of [[congenital heart disease]].  It refers to a combination of congenital [[atrial septal defect]] complicated by an acquired [[mitral stenosis]].
-==Classification==
 ==Pathophysiology==

v t e Congenital malformations and deformations of circulatory system (Q20-Q28, 745-747)
Cardiac chambers and connections	Persistent truncus arteriosus - Double outlet right ventricle (Taussig-Bing syndrome) - Transposition of the great vessels (dextro, levo)
Cardiac septa	Ventricular septal defect - Atrial septal defect (Lutembacher's syndrome) - Atrioventricular septal defect (Ostium primum) - Tetralogy of Fallot - Eisenmenger's syndrome
Right: pulmonary and tricuspid valves	pulmonary valves (stenosis, insufficiency) - tricuspid valves (stenosis, atresia) - Ebstein's anomaly
Left: aortic and mitral valves	aortic valves (stenosis, insufficiency, bicuspid) - mitral valves (stenosis, regurgitation) - Hypoplastic left heart syndrome
Other congenital malformations of heart	Dextrocardia - Levocardia - Cor triatriatum
Great arteries	aorta (Patent ductus arteriosus, Aortic coarctation, Interrupted aortic arch, Overriding aorta, Aneurysm of sinus of Valsalva, Vascular ring) - Pulmonary atresia
Great veins	Persistent left superior vena cava - Total anomalous pulmonary venous connection - Scimitar syndrome
Other	Arteriovenous malformation (Cerebral arteriovenous malformation)
See also non-congenital conditions (I, 390-459)