Arrhythmogenic right ventricular cardiomyopathy resident survival guide: Difference between revisions
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==Classification== | ==Classification== | ||
===Stages of disease=== | |||
*Concealed phase: Subclinical asymptomatic phase | |||
*Overt electrical disorder: Palpitations, syncope and typically with symptomatic ventricular arrhythmias of RV | |||
*RV failure: Progressive loss of RV myocardium due to fibro-fatty replacement impairs RV function, pump failure | |||
*Biventricular failure: Involvement of the interventricular septum and LV causing congestive heart failure (HF) | |||
===Patterns of expression=== | |||
==Causes== | ==Causes== | ||
Revision as of 15:13, 10 March 2015
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Steven Bellm, M.D. [2]
| Arrhythmogenic right ventricular cardiomyopathy resident survival guide Microchapters |
|---|
| Overview |
| Classification |
| Causes |
| FIRE |
| Diagnosis |
| Treatment |
| Do's |
| Dont's |
Overview
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a genetic disease characterized by myocyte loss and fibro-fatty tissue replacement of the right ventricular myocardium. This puts patients into risk of life-threatening ventricular arrhythmias and slowly progressive ventricular dysfunction. The diagnostic is challenging. Diagnosis of ARVC relays on a scoring system, with major or minor criteria on the Revised Task Force Criteria. Pharmacologic treatment of arrhythmias, catheter ablation of ventricular tachycardia, and ICD are main goals of the treatment.[1]
Classification
Stages of disease
- Concealed phase: Subclinical asymptomatic phase
- Overt electrical disorder: Palpitations, syncope and typically with symptomatic ventricular arrhythmias of RV
- RV failure: Progressive loss of RV myocardium due to fibro-fatty replacement impairs RV function, pump failure
- Biventricular failure: Involvement of the interventricular septum and LV causing congestive heart failure (HF)
Patterns of expression
Causes
Life Threatening Causes
Common Causes
FIRE: Focused Initial Rapid Evaluation
A Focused Initial Rapid Evaluation (FIRE) should be performed to identify patients in need of immediate intervention.
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Complete Diagnostic Approach
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Treatment
shown
hidden
Do's
Dont's
References
- ↑ Pinamonti B, Brun F, Mestroni L, Sinagra G (2014). "Arrhythmogenic right ventricular cardiomyopathy: From genetics to diagnostic and therapeutic challenges". World J Cardiol. 6 (12): 1234–44. doi:10.4330/wjc.v6.i12.1234. PMC 4278158. PMID 25548613.