Paraganglioma overview: Difference between revisions
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Paragangliomas are found predominantly in the abdomen (85%) and the thorax (12%), and only 3% are found in the head and neck region. Most occur as single tumors. When they occur in multiple sites they are usually found as a part of a heritable syndrome such as [[multiple endocrine neoplasia]] types II-A and II-B and [[SDH]]-related mutations. | Paragangliomas are found predominantly in the abdomen (85%) and the thorax (12%), and only 3% are found in the head and neck region. Most occur as single tumors. When they occur in multiple sites they are usually found as a part of a heritable syndrome such as [[multiple endocrine neoplasia]] types II-A and II-B and [[SDH]]-related mutations. | ||
==Historical perspective== | |||
Glomus tumor name formerly (and incorrectly) used paraganglioma. | |||
==Classification== | |||
Paraganglioma may be classified into several subtypes based on having neural cell line and site of origin. | |||
==References== | ==References== | ||
{{reflist|2}} | {{reflist|2}} | ||
{{Epithelial neoplasms}} | {{Epithelial neoplasms}} | ||
Revision as of 15:32, 31 August 2015
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
A paraganglioma is a rare neoplasm that can be found in the abdomen, thorax, and in the head and neck region. They are usually considered benign and complete surgical removal results in cure. However, in about 3% of cases they are malignant and have the ability to metastasize. Paragangliomas are still sometimes called glomus tumors (not to be confused with glomus tumors of the skin) and chemodectomas, but paraganglioma is the currently accepted and preferred term.
Paragangliomas are found predominantly in the abdomen (85%) and the thorax (12%), and only 3% are found in the head and neck region. Most occur as single tumors. When they occur in multiple sites they are usually found as a part of a heritable syndrome such as multiple endocrine neoplasia types II-A and II-B and SDH-related mutations.
Historical perspective
Glomus tumor name formerly (and incorrectly) used paraganglioma.
Classification
Paraganglioma may be classified into several subtypes based on having neural cell line and site of origin.