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| ==Treatment options== | | ==Treatment options== |
| An early diagnosis of cystic fibrosis and a comprehensive treatment plan can improve both survival and quality of life. Follow-up and monitoring are very important. If possible, patients should be cared for at cystic fibrosis specialty clinics, which can be found in many communities. When children reach adulthood, they should transfer to a cystic fibrosis specialty center for adults.
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| Treatment for lung problems includes:
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| * [[Antibiotics]] to prevent and treat lung and sinus infections. They may be taken by mouth, or given in the veins or by breathing treatments. People with cystic fibrosis may take antibiotics only when needed, or all the time. Doses are usually higher than normal. | |
| * Inhaled medicines to help open the airways
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| * [[DNAse enzyme replacement therapy]] to thin mucus and make it easier to cough up
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| * [[Flu vaccine]] and [[pneumococcal polysaccharide vaccine]] (PPV) yearly
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| * [[Lung transplant]] is an option in some cases
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| * [[Oxygen therapy]] may be needed as lung disease gets worse
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| Treatment for bowel and nutritional problems may include:
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| * A special diet high in protein and calories for older children and adults
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| * [[Pancreatic enzymes]] to help absorb fats and protein
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| * [[Vitamin supplements]], especially vitamins A, D, E, and K
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| * Your doctor can suggest other treatments if you have very hard stool
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| ==Where to find medical care for Cystic fibrosis?== | | ==Where to find medical care for Cystic fibrosis?== |
| [http://maps.google.com/maps?f=q&hl=en&geocode=&q={{urlencode:{{#if:{{{1|}}}|{{{1}}}|yourdisease}}}}&sll=37.0625,-95.677068&sspn=65.008093,112.148438&ie=UTF8&ll=37.0625,-95.677068&spn=91.690419,149.414063&z=2&source=embed Directions to Hospitals Treating Cystic fibrosis] | | [http://maps.google.com/maps?f=q&hl=en&geocode=&q={{urlencode:{{#if:{{{1|}}}|{{{1}}}|yourdisease}}}}&sll=37.0625,-95.677068&sspn=65.008093,112.148438&ie=UTF8&ll=37.0625,-95.677068&spn=91.690419,149.414063&z=2&source=embed Directions to Hospitals Treating Cystic fibrosis] |
| ==Prevention of Cystic fibrosis== | | ==Prevention of Cystic fibrosis== |
| There is no way to prevent cystic fibrosis. Screening those with a family history of the disease may detect the cystic fibrosis gene in 60 - 90% of carriers, depending on the test used.
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| ==What to expect (Outlook/Prognosis)?== | | ==What to expect (Outlook/Prognosis)?== |
| Most children with cystic fibrosis are fairly healthy until they reach adolescence or adulthood. They are able to participate in most activities and should be able to attend school. Many young adults with cystic fibrosis finish college or find employment.
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| Lung disease eventually worsens to the point where the person is disabled. Today, the average life span for people with cystic fibrosis who live to adulthood is approximately 35 years, a dramatic increase over the last three decades.
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| Death is usually caused by lung complications.
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| ==Possible complications== | | ==Possible complications== |
| The most common complication is chronic respiratory infection.
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| * Bowel problems, such as [[Gallstone disease (patient information)|gallstones]], [[intestinal obstruction]], and [[Rectal prolapse (patient information)|rectal prolapse]]
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| * [[Coughing up blood]]
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| * [[Chronic respiratory failure]]
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| * [[Diabetes]]
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| * [[Infertility]]
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| * [[Liver disease]] or [[liver failure]], [[Pancreatitis (patient information)|pancreatitis]], [[biliary cirrhosis]]
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| * [[Malnutrition]]
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| * [[Nasal polyps]] and sinusitis
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| * [[Osteoporosis (patient information)|Osteoporosis]] and [[arthritis]]
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| * Recurrent [[Pneumonia (patient information)|pneumonia]]
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| * [[Pneumothorax (patient information)|Pneumothorax]]
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| * Right-sided [[heart failure]] ([[cor pulmonale]])
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| ==Sources== | | ==Sources== |
| http://www.nlm.nih.gov/medlineplus/cysticfibrosis.html
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| http://www.nlm.nih.gov/medlineplus/ency/article/000107.htm
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| https://www.nhlbi.nih.gov/health-topics/cystic-fibrosis
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| [[Category:Gastroenterology]] | | [[Category:Gastroenterology]] |
| [[Category:Pediatrics]] | | [[Category:Pediatrics]] |
For the WikiDoc page for this topic, click here
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Assistant Editor-in-Chief: Meagan E. Doherty, Shaghayegh Habibi, M.D.[2]
Overview
What are the symptoms of Cystic fibrosis?
Symptoms in newborns
- Delayed growth
- Failure to gain weight during childhood
- No bowel movements in first 24 to 48 hours of life
- Salty-tasting skin
Symptoms related to bowel function
- Abdominal pain due to severe constipation
- Increased gas, bloating and distended abdomen
- Nausea and loss of appetite
- Pale or clay colored stool, foul smelling with mucus
- Weight loss
Symptoms related to the lungs and sinuses
What are the causes of Cystic fibrosis?
Who is at highest risk?
Diagnosis
Diseases with similar symptoms
When to seek urgent medical care?
Treatment options
Where to find medical care for Cystic fibrosis?
Directions to Hospitals Treating Cystic fibrosis
Prevention of Cystic fibrosis
What to expect (Outlook/Prognosis)?
Possible complications
Sources
Template:WikiDoc Sources