Sandbox:Hannan

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Hannan Javed, M.D.[2]

Overview

Vascular Anomalies
Vascular Tumors	Vascular Malformations
Benign Locally aggressive or Borderline Malignant	Simple	Combined°	of major named vessels	associated with other anomalies
	Capillary malformations Lymphatic malformations Venous malformations Arteriovenous malformations* Arteriovenous fistula*	Capillary venous malformation , Capillary lymphatic malformation Lymphatic venous malformation, Capillary lymphatic venous malformation Capillary arteriovenous malformation Capillary lymphatic arteriovenous malformation others	See details	See list

° defined as two or more vascular malformations found in one lesion

* high flow lesions

Classification

Classification of Vascular Tumors

Vascular tumors

Benign

Locally aggressive or borderline

Malignant

Infantile hemangioma / Hemangioma of infancy

Kaposiform hemangioendothelioma*

Angiosarcoma

Congenital hemangioma*

Retiform hemangioendothelioma

Epithelioid hemangioendothelioma

Tufted angioma*°

Papillary intralymphatic angioendothelioma (PILA), Dabska tumor

Others

Spindle-cell hemangioma

Composite hemangioendothelioma

Epithelioid hemangioma

Pseudomyogenic hemangioendothelioma

Pyogenic granuloma (also known as lobular capillary hemangioma)

Polymorphous hemangioendothelioma

Others Hobnail hemangioma Microvenular hemangioma Anastomosing hemangioma Glomeruloid hemangioma Papillary hemangioma Intravascular papillary endothelial hyperplasia Cutaneous epithelioid angiomatous nodule Acquired elastotic hemangioma Littoral cell hemangioma of the spleen

Hemangioendothelioma not otherwise specified

Related lesions Eccrine angiomatous hamartoma Reactive angioendotheliomatosis Bacillary angiomatosis

Kaposi sarcoma

Others

*congenital hemangioma (Rapidly involuting type) and tufted angioma may be associated with thrombocytopenia and/or consumptive coagulopathy in some cases.
°many experts consider tufted angioma and kaposiform hemangioendothelioma to be part of a spectrum rather than distinct entities

Vascular malformations

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Anomalies of major named vessels (also known as "channel type" or "truncal" vascular malformations)
Affect lymphatics veins arteries Anomalies of origin course number length diameter (aplasia, hypoplasia, stenosis, ectasia / aneurysm) valves communication (AVF) persistence (of embryonal vessel)

Combined vascular malformations*
CM + VM	capillary-venous malformation	CVM
CM + LM	capillary-lymphatic malformation	CLM
CM + AVM	capillary-arteriovenous malformation	CAVM
LM + VM	lymphatic-venous malformation	LVM
CM + LM + VM	capillary-lymphatic-venous malformation	CLVM
CM + LM + AVM	capillary-lymphatic-arteriovenous malformation	CLAVM
CM + VM + AVM	capillary-venous-arteriovenous malformation	CVAVM
CM + LM + VM + AVM	capillary-lymphatic-venous-arteriovenous m.	CLVAVM

Vascular malformations associated with other anomalies
Klippel-Trenaunay syndrome *
Parkes Weber syndrome
Servelle-Martorell syndrome
Sturge-Weber syndrome
Limb CM + congenital non-progressive limb overgrowth
Maffucci syndrome
Macrocephaly-CM (M-CM / MCAP) *
Microcephaly-CM (MICCAP)
CLOVES syndrome *
Proteus syndrome
Bannayan-Riley-Ruvalcaba sd

Pathogenesis of xxx disease is due to:

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  2. vvv