Lymphangioma (patient information): Difference between revisions

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=== Histochemical staining: ===
=== Histochemical staining: ===
* Histochemical staining is recommended to document [[lymphangioma]].<ref name="SauterFoedinger2016">{{cite journal|last1=Sauter|first1=Birthe|last2=Foedinger|first2=Dagmar|last3=Sterniczky|first3=Barbara|last4=Wolff|first4=Klaus|last5=Rappersberger|first5=Klemens|title=Immunoelectron Microscopic Characterization of Human Dermal Lymphatic Microvascular Endothelial Cells: Differential Expression of CD31, CD34, and Type IV Collagen with Lymphatic Endothelial Cells vs Blood Capillary Endothelial Cells in Normal Human Skin, Lymphangioma, and Hemangioma In Situ|journal=Journal of Histochemistry & Cytochemistry|volume=46|issue=2|year=2016|pages=165–176|issn=0022-1554|doi=10.1177/002215549804600205}}</ref>
* Histochemical staining is recommended to document [[lymphangioma]].


=== MRI: ===
=== MRI: ===
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==Treatment options==
==Treatment options==
Medical Therapy


There is no medical treatment for lymphangioma; the mainstay of therapy is surgery.
==== Medical Therapy: ====
Surgery
There is no medical treatment for lymphangioma; the mainstay of therapy is surgery.  
 
===== Surgery: =====
The mainstay of therapy for lymphangioma is surgery. Treatment for lymphangioma involves the removal of the abnormal tissue; however complete removal may be impossible without removing other normal areas. Most patients need at least two procedures done for the removal process to be achieved.  
The mainstay of therapy for lymphangioma is surgery. Treatment for lymphangioma involves the removal of the abnormal tissue; however complete removal may be impossible without removing other normal areas. Most patients need at least two procedures done for the removal process to be achieved.  


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==What to expect (Outlook/Prognosis)?==
==What to expect (Outlook/Prognosis)?==
Prognosis of lymphangioma is generally excellent after surgical intervention.  
Prognosis of lymphangioma is generally good after surgical intervention.  


==Possible complications==
==Possible complications==
*Common [[complications]] of [[lymphangiomas]] are primarily associated to the location of lesion.<ref name="pmid10712360">{{cite journal |vauthors=Faul JL, Berry GJ, Colby TV, Ruoss SJ, Walter MB, Rosen GD, Raffin TA |title=Thoracic lymphangiomas, lymphangiectasis, lymphangiomatosis, and lymphatic dysplasia syndrome |journal=Am. J. Respir. Crit. Care Med. |volume=161 |issue=3 Pt 1 |pages=1037–46 |date=March 2000 |pmid=10712360 |doi=10.1164/ajrccm.161.3.9904056 |url=}}</ref>
*Common [[complications]] of [[lymphangiomas]] are primarily associated to the location of lesion.
*Growth of lesion causes compressive effects on surrounding tissues. Which include following:<ref name="pmid4537032">{{cite journal |vauthors=Runyon BA, Forker EL, Sopko JA |title=Pleural-fluid kinetics in a patient with primary lymphedema, pleural effusions, and yellow nails |journal=Am. Rev. Respir. Dis. |volume=119 |issue=5 |pages=821–5 |date=May 1979 |pmid=453703 |doi=10.1164/arrd.1979.119.5.821 |url=}}</ref>
*Growth of lesion causes compressive effects on surrounding tissues. Which include following:
**[[Dyspnea]]: Trachea<ref name="pmid8444562" />  
**[[Dyspnea]]: Trachea<ref name="pmid8444562" />  
**[[Dysphagia]]: Esophagous<ref name="pmid40657002">{{cite journal |vauthors=Duhra PM, Quigley EM, Marsh MN |title=Chylous ascites, intestinal lymphangiectasia and the 'yellow-nail' syndrome |journal=Gut |volume=26 |issue=11 |pages=1266–9 |date=November 1985 |pmid=4065700 |pmc=1432907 |doi= |url=}}</ref>
**[[Dysphagia]]: Esophagous  
**[[Constipation]]: Gastrointestinal tract<ref name="pmid4065700">{{cite journal |vauthors=Duhra PM, Quigley EM, Marsh MN |title=Chylous ascites, intestinal lymphangiectasia and the 'yellow-nail' syndrome |journal=Gut |volume=26 |issue=11 |pages=1266–9 |date=November 1985 |pmid=4065700 |pmc=1432907 |doi= |url=}}</ref>
**[[Constipation]]: Gastrointestinal tract
**[[Diplopia]] and [[proptosis]]: Retro-orbital tissue of [[eye]]<ref name="pmid453703">{{cite journal |vauthors=Runyon BA, Forker EL, Sopko JA |title=Pleural-fluid kinetics in a patient with primary lymphedema, pleural effusions, and yellow nails |journal=Am. Rev. Respir. Dis. |volume=119 |issue=5 |pages=821–5 |date=May 1979 |pmid=453703 |doi=10.1164/arrd.1979.119.5.821 |url=}}</ref>
**[[Diplopia]] and [[proptosis]]: Retro-orbital tissue of [[eye]]
**[[Wheeze]]: Lower Respiratory tract<ref name="pmid8977864">{{cite journal |vauthors=Papsin BC, Evans JN |title=Isolated laryngeal lymphangioma: a rare cause of airway obstruction in infants |journal=J Laryngol Otol |volume=110 |issue=10 |pages=969–72 |date=October 1996 |pmid=8977864 |doi= |url=}}</ref>
**[[Wheeze]]: Lower Respiratory tract
**[[Chest pain|Chest Pain]]: Mediastinum
**[[Chest pain|Chest Pain]]: Mediastinum
**[[Shortness of breath|Shortness of breadth]]: [[Lung|Lungs]]<ref name="pmid8444562">{{cite journal |vauthors=Williams WT, Cole RR |title=Lymphangioma presenting as congenital stridor |journal=Int. J. Pediatr. Otorhinolaryngol. |volume=26 |issue=2 |pages=185–91 |date=March 1993 |pmid=8444562 |doi= |url=}}</ref>
**[[Shortness of breath|Shortness of breadth]]: [[Lung|Lungs]]  
**Bladder Obstruction: [[Urinary tract]]
**Bladder Obstruction: [[Urinary tract]]
**Bone loss or overgrowth: Skeletal tissue<ref name="pmid9473098">{{cite journal |vauthors=Ogita S, Deguchi E, Tokiwa K, Iwata J, Kubota Y, Iwai N |title=Ongoing osteolysis in patients with lymphangioma |journal=J. Pediatr. Surg. |volume=33 |issue=1 |pages=45–8 |date=January 1998 |pmid=9473098 |doi= |url=}}</ref>
**Bone loss or overgrowth: Skeletal tissue
**[[Inflammation]] or [[bleeding]] into the lesion
**[[Inflammation]] or [[bleeding]] into the lesion
**Recurrent [[Cellulitis]]:Visible deformity<ref name="pmid14395215">{{cite journal |vauthors=MANN TP |title=Hemihypertrophy left side of body; congenital lymphatic oedema of left arm; radiological enlargement of heart shadow |journal=Proc. R. Soc. Med. |volume=48 |issue=5 |pages=330–1 |date=May 1955 |pmid=14395215 |pmc=1918895 |doi= |url=}}</ref>
**Recurrent [[Cellulitis]]:Visible deformity


==Source==
==Source==
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[[Category:Medicine]]
[[Category:Medicine]]
[[Category:Vascular medicine]]
[[Category:Vascular medicine]]
<references />

Revision as of 14:10, 1 November 2018

For the WikiDoc page on this topic, click here

Lymphangioma

Overview

What are the symptoms?

What are the causes?

Who is at highest risk?

Diagnosis

When to seek urgent medical care?

Treatment options

Where to find medical care for Lymphangioma?

Prevention

What to expect (Outlook/Prognosis)?

Possible complications

Lymphangioma On the Web

Ongoing Trials at Clinical Trials.gov

Images of Lymphangioma

Videos on Lymphangioma

FDA on Lymphangioma

CDC on Lymphangioma

Lymphangioma in the news

Blogs on Lymphangioma

Directions to Hospitals Treating Lymphangioma

Risk calculators and risk factors for Lymphangioma

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]Badria Munir M.B.B.S.[2]

Overview

Lymphangioma is abnormality of lymph vessels, which are normally involved in the re-circulation of excess body fluid back into the blood stream. The exact pathogenesis of lymphangioma is not fully understood. It is thought that lymphangioma is caused by either sequestration of lymph tissue, abnormal budding of lymph vessels, lack of fusion with the venous system, or obstruction of lymph vessels. Lymphangiomas most commonly develop at the head and neck regions.

What are the symptoms of Lymphangioma?

  • The majority of patients with lymphangioma are asymptomatic.
  • As the mass increases in size, lymphangioma patients may develop site-specific symptoms, such as:

What causes Lymphangioma?

Who is at highest risk?

The most potent risk factor in the development of lymphangioma is the presence of genetic disorders such as Turner syndrome, Down syndrome, and Noonan syndrome.[1]

Diagnosis

Biopsy:

Histochemical staining:

  • Histochemical staining is recommended to document lymphangioma.

MRI:

  • MRI is primarily used for the diagnosis of lymphangioma.
  • MRI can mar the degree of involvement and extent of lesion.
  • MRI can prevent extensive, incomplete surgical resection, because poorly removed lesion can lead to recurrence.

When to seek urgent medical care?

In cases of severe complications of disease, such as

  • Difficulty breathing
  • Difficulty swallowing

Treatment options

Medical Therapy:

There is no medical treatment for lymphangioma; the mainstay of therapy is surgery.

Surgery:

The mainstay of therapy for lymphangioma is surgery. Treatment for lymphangioma involves the removal of the abnormal tissue; however complete removal may be impossible without removing other normal areas. Most patients need at least two procedures done for the removal process to be achieved.

Where to find medical care for Lymphangioma?

Directions to Hospitals Treating Lymphangioma

Prevention of Lymphangioma

There are no established measures for the primary prevention of lymphangioma.

What to expect (Outlook/Prognosis)?

Prognosis of lymphangioma is generally good after surgical intervention.

Possible complications

Source

Template:WH Template:WS

  1. ↑ Invalid <ref> tag; no text was provided for refs named pmid21938186
  2. ↑ Invalid <ref> tag; no text was provided for refs named pmid8444562
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