Acroangiodermatitis: Difference between revisions
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Acroangiodermatitis is a rare skin condition characterised by [[hyperplasia]] of pre-existing [[vasculature]] due to venous [[hypertension]] from severe chronic venous stasis. It is associated with [[amputee]]s, [[haemodialysis]] (HD) patients with arteriovenous (AV) shunts, and patients with paralysed legs, [[hepatitis C]], [[chronic venous insufficiency]] or AV malformations (AVM). Patients present with itchy, painful, confluent, violaceous or brown-black macules, papules or plaques usually at the distal lower limbs. There may be ulceration and bleeding. The histologic features are capillary proliferation and perivascular inflammation involving eosinophils in the dermis with minimal epidermal changes. Management includes [[compression therapy]], wound care and surgical correction of AVM. [[Dapsone]] combined with leg elevation and compression, and erythromycin for HD patients with AV fistulas have also been reported. The lesions may persist for years with complications like [[ulcer]]ation, bleeding and infection. | Acroangiodermatitis is a rare skin condition characterised by [[hyperplasia]] of pre-existing [[vasculature]] due to venous [[hypertension]] from severe chronic venous stasis. It is associated with [[amputee]]s, [[haemodialysis]] (HD) patients with arteriovenous (AV) shunts, and patients with paralysed legs, [[hepatitis C]], [[chronic venous insufficiency]] or AV malformations (AVM). Patients present with itchy, painful, confluent, violaceous or brown-black macules, papules or plaques usually at the distal lower limbs. There may be ulceration and bleeding. The histologic features are capillary proliferation and perivascular inflammation involving eosinophils in the dermis with minimal epidermal changes. Management includes [[compression therapy]], wound care and surgical correction of AVM. [[Dapsone]] combined with leg elevation and compression, and erythromycin for HD patients with AV fistulas have also been reported. The lesions may persist for years with complications like [[ulcer]]ation, bleeding and infection. | ||
== Differential Diagnosis == | |||
Acroangiodermatitis should be differentiated from other conditions presenting as purplish-blue to brown papules and plaques on extremities. The differentials include the following: | |||
==Physical examination== | ==Physical examination== | ||
Revision as of 04:41, 7 January 2019
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Jesus Rosario Hernandez, M.D. [2].
Synonyms and keywords: Mali acroangiodermatitis; Pseudo-Kaposi's sarcoma.
Overview
Acroangiodermatitis of Mali (also known as "Mali acroangiodermatitis" and "Pseudo-Kaposi's sarcoma"[1]) is a rare cutaneous condition often characterized by purplish-blue to brown papules and plaques on the medial and lateral malleolus of both legs.[1]:1604[2]
Acroangiodermatitis is a rare skin condition characterised by hyperplasia of pre-existing vasculature due to venous hypertension from severe chronic venous stasis. It is associated with amputees, haemodialysis (HD) patients with arteriovenous (AV) shunts, and patients with paralysed legs, hepatitis C, chronic venous insufficiency or AV malformations (AVM). Patients present with itchy, painful, confluent, violaceous or brown-black macules, papules or plaques usually at the distal lower limbs. There may be ulceration and bleeding. The histologic features are capillary proliferation and perivascular inflammation involving eosinophils in the dermis with minimal epidermal changes. Management includes compression therapy, wound care and surgical correction of AVM. Dapsone combined with leg elevation and compression, and erythromycin for HD patients with AV fistulas have also been reported. The lesions may persist for years with complications like ulceration, bleeding and infection.
Differential Diagnosis
Acroangiodermatitis should be differentiated from other conditions presenting as purplish-blue to brown papules and plaques on extremities. The differentials include the following:
Physical examination
Gallery
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Acroangiodermatitis.
Adapted from [http://www.atlasdermatologico.com.br/disease.jsf?diseaseId=9 -
Acroangiodermatitis.
Adapted from [http://www.atlasdermatologico.com.br/disease.jsf?diseaseId=9 -
Acroangiodermatitis.
Adapted from [http://www.atlasdermatologico.com.br/disease.jsf?diseaseId=9
References
- ↑ 1.0 1.1 Rapini, Ronald P.; Bolognia, Jean L.; Jorizzo, Joseph L. (2007). Dermatology: 2-Volume Set. St. Louis: Mosby. ISBN 1-4160-2999-0.
- ↑ Scholz S, Schuller-Petrovic S, Kerl H (March 2005). "Mali acroangiodermatitis in homozygous activated protein C resistance". Arch Dermatol. 141 (3): 396–7. doi:10.1001/archderm.141.3.396. PMID 15781687.