Caroli's disease overview: Difference between revisions
No edit summary |
Agnesrinky (talk | contribs) |
||
| Line 4: | Line 4: | ||
== Overview == | == Overview == | ||
Caroli disease is a rare inherited disorder characterized by dilatation of the intrahepatic bile ducts. There are two types of Caroli disease, the most common being the simple, or isolated case where the bile ducts are widened by [[ectasia]]. The second, more complex, cause is commonly known as Caroli Syndrome. This complex form is also linked with portal [[hypertension]] and [[congenital hepatic fibrosis]]. | [[Caroli disease]] is a rare [[inherited disorder]] characterized by dilatation of the [[intrahepatic bile ducts]]. There are two types of [[Caroli disease]], the most common being the simple, or isolated case where the [[bile ducts]] are widened by [[ectasia]]. The second, more complex, cause is commonly known as [[Caroli Syndrome]]. This complex form is also linked with portal [[hypertension]] and [[congenital hepatic fibrosis]]. | ||
<ref name=Karim>{{cite journal |author=Karim B |title=Caroli’s Disease Case Reports |journal=Indian Pediatrics |volume=41 |issue= 8|pages=848–50 |month=August |year=2007 |url=http://www.indianpediatrics.net/aug2004/848.pdf|format=PDF |pmid=15347876}}</ref> The differences between the causes of the two cases have not yet been discovered. Caroli disease is also associated with [[liver failure]] and [[polycystic kidney disease]]. | <ref name=Karim>{{cite journal |author=Karim B |title=Caroli’s Disease Case Reports |journal=Indian Pediatrics |volume=41 |issue= 8|pages=848–50 |month=August |year=2007 |url=http://www.indianpediatrics.net/aug2004/848.pdf|format=PDF |pmid=15347876}}</ref> The differences between the causes of the two cases have not yet been discovered. [[Caroli disease]] is also associated with [[liver failure]] and [[polycystic kidney disease]]. | ||
<ref name=EMedRad>{{EMedicine|radio|131|Romano WJ: Caroli Disease}}</ref> | <ref name=EMedRad>{{EMedicine|radio|131|Romano WJ: Caroli Disease}}</ref> | ||
Caroli disease also is known as communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic [[biliary tree]]. Caroli disease is distinct from other diseases that cause ductal dilatation caused by obstruction, in that it is not one of the many [[choledochal cyst]] derivatives. | [[Caroli disease]] also is known as communicating [[cavernous]] [[ectasia]], or congenital cystic dilatation of the intrahepatic [[biliary tree]]. [[Caroli disease]] is distinct from other diseases that cause ductal dilatation caused by obstruction, in that it is not one of the many [[choledochal cyst]] derivatives. | ||
<ref name=Karim/> | <ref name=Karim/> | ||
Revision as of 17:56, 2 March 2022
|
Caroli's disease Microchapters |
|
Diagnosis |
|---|
|
Treatment |
|
Case Studies |
|
Caroli's disease overview On the Web |
|
American Roentgen Ray Society Images of Caroli's disease overview |
|
Risk calculators and risk factors for Caroli's disease overview |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Caroli disease is a rare inherited disorder characterized by dilatation of the intrahepatic bile ducts. There are two types of Caroli disease, the most common being the simple, or isolated case where the bile ducts are widened by ectasia. The second, more complex, cause is commonly known as Caroli Syndrome. This complex form is also linked with portal hypertension and congenital hepatic fibrosis. [1] The differences between the causes of the two cases have not yet been discovered. Caroli disease is also associated with liver failure and polycystic kidney disease. [2]
Caroli disease also is known as communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic biliary tree. Caroli disease is distinct from other diseases that cause ductal dilatation caused by obstruction, in that it is not one of the many choledochal cyst derivatives. [1]
References
- ↑ 1.0 1.1 Karim B (2007). "Caroli's Disease Case Reports" (PDF). Indian Pediatrics. 41 (8): 848–50. PMID 15347876. Unknown parameter
|month=ignored (help) - ↑ Romano WJ: Caroli Disease at eMedicine