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| {{CMG}}
| | #REDIRECT [[Bile duct cyst]] |
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| {{Editor Help}}
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| ==Overview==
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| {{Infobox_Disease
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| | Name = {{PAGENAME}}
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| | Image =
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| | Caption =
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| | DiseasesDB = 2527
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| | ICD10 = {{ICD10|Q|44|4|q|38}}
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| | ICD9 = {{ICD9|751.69}}
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| | ICDO =
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| | OMIM =
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| | MedlinePlus =
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| | eMedicineSubj = med
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| | eMedicineTopic = 349
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| | MeshID = D015529
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| }}
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| '''Choledochal cysts''' are [[congenital]] conditions associated with [[benign]] [[cyst]]ic dilatation of [[bile ducts]]. They are uncommon in western countries<ref name="pmid17825168">{{cite journal |author=Liu YB, Wang JW, Devkota KR, ''et al'' |title=Congenital choledochal cysts in adults: twenty-five-year experience |journal=Chin. Med. J. |volume=120 |issue=16 |pages=1404–7 |year=2007 |pmid=17825168 |doi=}}</ref> but not as rare in East Asian nations like Japan and China.
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| ==Genetics==
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| Choledochal cysts may be associated with [[Caroli disease]].
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| ==Classification scheme==
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| Choledochal cysts were classified into 5 types by Todani in 1977<ref>{{cite journal |author=Todani T, Watanabe Y, Narusue M, Tabuchi K, Okajima K |title=Congenital bile duct cysts: Classification, operative procedures, and review of thirty-seven cases including cancer arising from choledochal cyst |journal=Am. J. Surg. |volume=134 |issue=2 |pages=263-9 |year=1977 |pmid=889044}}</ref>.
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| [[Image:Choledochal_cysts.png|thumb|300px|center|Different types of choledochal cysts]]
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| Classification was based on site of the cyst or dilatation. Type I to IV has been subtyped.
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| *'''Type I:''' Most common variety involving saccular or fusiform dilatation of a portion or entire [[common bile duct]] (CBD) with normal intrahepatic duct.
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| *'''Type II:''' Isolated diverticulum protruding from the CBD.
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| *'''Type III or Choledochocele:''' Arise from dilatation of duodenal portion of CBD or where pancreatic duct meets.
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| *'''Type IV:''' Dilatation of both intrahepatic and extrahepatic biliary duct.
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| *'''Type V''' or '''Caroli's disease:''' Cystic dilatation of intra hepatic biliary ducts.
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| ==Signs and Symptoms==
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| Most of them present in 1st year of life; adult presentation is rare and usually at this stage is associated with complication . Classic triad of ''intermittent abdominal pain, [[jaundice]], and a [[right upper quadrant]] [[abdominal mass]]'' is found only in minority of patients. A hepatic cyst may be present, as may short stature. A fever of unknown origin may be observed. [[Pancreatitis]] may be present.
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| ==Treatments==
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| Choledochal cysts are treated by surgical excision of the cyst with the formation of a [[roux-en-Y]] anastamosis to the [[biliary duct]].
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| Future complications include [[cholangitis]] and a 2% risk of malignancy, which may develop in any part of the biliary tree.
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| ==References==
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| <references />
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| {{SIB}}
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| {{Cystic diseases}}
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| {{Congenital malformations and deformations of digestive system}}
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| [[Category:Gastroenterology]]
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| [[pl:Torbiele dróg żółciowych]]
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