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{{Infobox_Disease |
{{Infobox_Disease |
   Name          = {{PAGENAME}} |
   Name          = {{PAGENAME}} |
  Image          = Interrupted aortic arch.png|
  Caption        = Hemorrhagic Necrosis; Massive, Postoperative: Gross; natural color, heart, in situ, a 2 day old infant, operative death, interrupted aortic arch and [[VSD]] <br> <small> [http://www.peir.net Image courtesy of Professor Peter Anderson DVM PhD and published with permission © PEIR, University of Alabama at Birmingham, Department of Pathology] </small>|
   DiseasesDB    = |
   DiseasesDB    = |
   ICD10          = {{ICD10|Q|25|2|q|20}} ([[EUROCAT]]) |
   ICD10          = {{ICD10|Q|25|2|q|20}} ([[EUROCAT]]) |
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   MeshID        = |
   MeshID        = |
}}
}}
{{SI}}
{{Interrupted aortic arch}}
{{WikiDoc Cardiology Network Infobox}}
 
{{CMG}}
{{CMG}}


'''Associate Editor-In-Chief:''' {{CZ}}
'''Associate Editor-In-Chief:''' {{CZ}}, [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu], [[Priyamvada Singh|Priyamvada Singh, MBBS]] [[mailto:psingh@perfuse.org]]


'''Associate Editor-in-Chief:''' [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu]
'''Assistant Editor-In-Chief:''' [[Kristin Feeney|Kristin Feeney, B.S.]] [[mailto:kfeeney@perfuse.org]]
==[[Interrupted aortic arch overview|Overview]]==


{{Editor Join}}
==[[Interrupted aortic arch pathophysiology|Pathophysiology]]==


==Overview==
==[[Interrupted aortic arch epidemiology and demographics|Epidemiology and demographics]]==
'''Interrupted aortic arch''' is a very rare heart defect in which the [[aorta]] is not completely developed. There is a gap between the ascending and descending thoracic aorta. Almost all patients also have other cardiac anomalies. It can be diagnosed with an [[echocardiogram]]. Treatment consists of [[open heart surgery]] soon after birth. Awaiting surgery, [[prostaglandin]] can be administered to keep the [[ductus arteriosus]] open, thereby allowing blood flow to the lower body.


*Interrupted aortic arch (IAA) is a separation between the ascending and descending aortas. There are 3 types of this abnormality:
==[[Interrupted aortic arch natural history|Natural history, Complications, and Prognosis]]==
:*Type A: Interruption is distal to the subclavian artery
 
:*Type B: Interruption occurs between the second carotid and the ipsilateral subclavian arteries
==[[Interrupted aortic arch causes|Causes]]==
:*Type C: Interruption occurs between two carotid arteries.
 
*Each type is divided into 3 subtypes:
==[[Interrupted aortic arch differential diagnosis|Differentiating Interrupted aortic arch from other Disorders]]==
:*Subtype 1: Normal subclavian artery
 
:*Subtype 2: Aberrant subclavian artery
==Diagnosis==
:*Subtype 3: Isolated subclavian artery that arises from the ductus arteriosus.
[[Interrupted aortic arch history and symptoms|History and Symptoms]] | [[Interrupted aortic arch physical examination|Physical Examination]] | [[Interrupted aortic arch laboratory tests|Laboratory Tests]] | [[Interrupted aortic arch electrocardiogram | Electrocardiogram]] | [[Interrupted aortic arch chest x ray|Chest X Ray]] | [[Interrupted aortic arch MRI|MRI]] | [[Interrupted aortic arch CT|CT]] | [[Interrupted aortic arch echocardiography|Echocardiography]] | [[Interrupted aortic arch other imaging findings|Other Imaging Findings]] | [[Interrupted aortic arch other diagnostic studies|Other Diagnostic Studies]]
*In addition to the type of IAA, the following information is important for surgical planning
 
:*Evaluation of the distance between the proximal and distal segments,
==Treatment==
:*Size of a [[patent ductus arteriosus]]
'''Medical:''' [[Interrupted aortic arch medical therapy|Medical Therapy]]
:*Narrowest dimension of the left ventricular outflow tract
 
:*Other cardiac structural abnormalities are important for surgical planning.
'''Surgical:''' [[Interrupted aortic arch surgery|Surgery]]
*A right-sided descending aorta with aortic interruption is almost always associated with [[DiGeorge syndrome]].
 
[[Interrupted aortic arch primary prevention|Primary Prevention]] | [[Interrupted aortic arch secondary prevention|Secondary Prevention]] | [[Interrupted aortic arch cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Interrupted aortic arch future or investigational therapies|Future or Investigational Therapies]]
 
==References==
{{reflist}}


==External links==
==External links==
Line 48: Line 50:


==Additional Reading==
==Additional Reading==
* Hyun Woo Goo, In-Sook Park, Jae Kon Ko, Yong Hwue Kim, Dong-Man Seo, Tae-Jin Yun, Jeong-Jun Park, and Chong Hyun Yoon. CT of Congenital Heart Disease: Normal Anatomy and Typical Pathologic Conditions. RadioGraphics 2003 23: S147-165S.  
* Hyun Woo Goo, In-Sook Park, Jae Kon Ko, Yong Hwue Kim, Dong-Man Seo, Tae-Jin Yun, Jeong-Jun Park, and Chong Hyun Yoon. CT of Congenital Heart Disease: Normal Anatomy and Typical Pathologic Conditions. RadioGraphics 2003 23: S147-165S.  
* Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843
* Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843


{{Congenital malformations and deformations of circulatory system}}
[[Category:Cardiovascular system]]
{{SIB}}
[[Category:Cardiology]]
[[Category:Cardiology]]
[[Category:Congenital heart disease]]
[[Category:Congenital heart disease]]
[[Category:Pediatrics]]
[[Category:Pulmonology]]


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Revision as of 19:30, 15 July 2011

For patient information click here

Interrupted aortic arch
ICD-10 Q25.2 (EUROCAT)
ICD-9 747.11
eMedicine ped/2515 

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2], Keri Shafer, M.D. [3], Priyamvada Singh, MBBS [[4]]

Assistant Editor-In-Chief: Kristin Feeney, B.S. [[5]]

Overview

Pathophysiology

Epidemiology and demographics

Natural history, Complications, and Prognosis

Causes

Differentiating Interrupted aortic arch from other Disorders

Diagnosis

History and Symptoms | Physical Examination | Laboratory Tests | Electrocardiogram | Chest X Ray | MRI | CT | Echocardiography | Other Imaging Findings | Other Diagnostic Studies

Treatment

Medical: Medical Therapy

Surgical: Surgery

Primary Prevention | Secondary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies

References

External links

Additional Reading

  • Hyun Woo Goo, In-Sook Park, Jae Kon Ko, Yong Hwue Kim, Dong-Man Seo, Tae-Jin Yun, Jeong-Jun Park, and Chong Hyun Yoon. CT of Congenital Heart Disease: Normal Anatomy and Typical Pathologic Conditions. RadioGraphics 2003 23: S147-165S.
  • Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843

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