Noncompaction cardiomyopathy natural history: Difference between revisions
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** [[Muscular dystrophy|Myotubular cardiomyopathy]] | ** [[Muscular dystrophy|Myotubular cardiomyopathy]] | ||
** [[Barth syndrome]] | ** [[Barth syndrome]] | ||
==Prognosis== | |||
In so far as noncompaction cardiomyopathy is a relatively new disease, it's impact on the human life expectancy is not very well understood. In a 2005 study <ref name= Oechslin>{{Cite journal | last =Oechslin| first =Erwin | last2 =Jenni | first2 =Rolf | title = Non-compaction of the Left Ventricular Myocardium - From Clinical Observation to the Discovery of a New Disease | journal = | publisher = | volume = | issue =| pages = | year = 2005| url= http://www.touchcardiology.com/compaction-left-ventricular-myocardium-a352-3.html| format = webpage | id =}}</ref> which documented the long term follow up of 34 patients with NCC, 35% had died at the age of 42 +/- 40 months with a further 12% having to under go a heart transplant due to heart failure. However, this study was based upon symptomatic patients referred to a tertiary care center, and so were suffering from more severe forms of NCC than might be found typically in the population. As NCC is a genetic disease, as a precaution immediate family members are being tested which is turning up more supposedly healthy people with NCC who are not suffering from it. The long term prognosis for these people is currently unknown. | |||
==References== | ==References== | ||
Revision as of 02:34, 3 August 2011
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Noncompaction Cardiomyopathy Microchapters |
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Pathophysiology |
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Differentiating Noncompaction Cardiomyopathy from other Diseases |
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Noncompaction cardiomyopathy natural history On the Web |
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Risk calculators and risk factors for Noncompaction cardiomyopathy natural history |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
The presence of NCC can also lead to other complications around the heart and in other organs. These are not necessarily common complications and no paper has yet to document the incidence of these complicationcs.
- Heart Related
- Abnormalities of the origin of the left coronary artery
- Pulmonary atresia
- Stenosis
- Right or Left ventricle obstruction
- Hypoplastic left ventricle
- Mitral regurgitation
- Tachyarrhythmias and sudden cardiac death
- Thrombus in the left ventricle
- Neuromuscular (Pertaining to both nerves and muscles)
- Genetic related
Prognosis
In so far as noncompaction cardiomyopathy is a relatively new disease, it's impact on the human life expectancy is not very well understood. In a 2005 study [1] which documented the long term follow up of 34 patients with NCC, 35% had died at the age of 42 +/- 40 months with a further 12% having to under go a heart transplant due to heart failure. However, this study was based upon symptomatic patients referred to a tertiary care center, and so were suffering from more severe forms of NCC than might be found typically in the population. As NCC is a genetic disease, as a precaution immediate family members are being tested which is turning up more supposedly healthy people with NCC who are not suffering from it. The long term prognosis for these people is currently unknown.
References
- ↑ Oechslin, Erwin; Jenni, Rolf (2005). "Non-compaction of the Left Ventricular Myocardium - From Clinical Observation to the Discovery of a New Disease" (webpage).