Noncompaction cardiomyopathy echocardiography: Difference between revisions
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On echocardiography there is ventricular hypertrophy with deep recesses which tend to be located apically <ref>Weiford BC, Subbarao VD, Mulhern KM, Noncompaction of the ventricular myocardium. Circulation 109 (24): 2965-71 2004</ref>. | On echocardiography there is ventricular hypertrophy with deep recesses which tend to be located apically <ref>Weiford BC, Subbarao VD, Mulhern KM, Noncompaction of the ventricular myocardium. Circulation 109 (24): 2965-71 2004</ref>. | ||
==Echocardiographic findings== | ==Echocardiographic findings<ref>.Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.</ref>== | ||
*There are deep trabeculations in the ventricular wall | *There are deep trabeculations in the ventricular wall | ||
*There is systolic dysfunction with an average LVEF of 33% | *There is systolic dysfunction with an average LVEF of 33% | ||
*There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictie filling pattern | *It is notable that there is hypokinesis in both the noncompacted as well as the compacted segments. It has been speculated that this is due to the microcirculatory defect observed in these patients. | ||
*There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictie filling pattern. | |||
*The left ventricular wall is thick with a two layered appearance | *The left ventricular wall is thick with a two layered appearance | ||
*The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick | *The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick | ||
*The ratio of the non-compacted endocardial layer to the epicardial layer is > 2 in adults and >1.4 in children | *The ratio of the non-compacted endocardial layer to the epicardial layer is > 2 in adults and >1.4 in children | ||
*41% of patients will have involvement of the RV apex | *41% of patients will have involvement of the RV apex | ||
==References== | ==References== | ||
Revision as of 14:03, 7 August 2011
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
On echocardiography there is ventricular hypertrophy with deep recesses which tend to be located apically [1].
Echocardiographic findings[2]
- There are deep trabeculations in the ventricular wall
- There is systolic dysfunction with an average LVEF of 33%
- It is notable that there is hypokinesis in both the noncompacted as well as the compacted segments. It has been speculated that this is due to the microcirculatory defect observed in these patients.
- There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictie filling pattern.
- The left ventricular wall is thick with a two layered appearance
- The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick
- The ratio of the non-compacted endocardial layer to the epicardial layer is > 2 in adults and >1.4 in children
- 41% of patients will have involvement of the RV apex
References
- ↑ Weiford BC, Subbarao VD, Mulhern KM, Noncompaction of the ventricular myocardium. Circulation 109 (24): 2965-71 2004
- ↑ .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.