Noncompaction cardiomyopathy echocardiography: Difference between revisions
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/* Echocardiographic findings.Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493 |
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*There is systolic dysfunction with an average LVEF of 33% | *There is systolic dysfunction with an average LVEF of 33% | ||
*It is notable that there is hypokinesis in both the noncompacted as well as the compacted segments. It has been speculated that this is due to the microcirculatory defect observed in these patients. | *It is notable that there is hypokinesis in both the noncompacted as well as the compacted segments. It has been speculated that this is due to the microcirculatory defect observed in these patients. | ||
*There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a | *There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictive filling pattern. | ||
*The left ventricular wall is thick with a two layered appearance | *The left ventricular wall is thick with a two layered appearance | ||
*The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick | *The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick | ||
Revision as of 14:05, 7 August 2011
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Noncompaction Cardiomyopathy Microchapters |
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Pathophysiology |
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Differentiating Noncompaction Cardiomyopathy from other Diseases |
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Diagnosis |
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Treatment |
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Noncompaction cardiomyopathy echocardiography On the Web |
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Risk calculators and risk factors for Noncompaction cardiomyopathy echocardiography |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
On echocardiography there is ventricular hypertrophy with deep recesses which tend to be located apically [1].
Echocardiographic findings[2]
- There are deep trabeculations in the ventricular wall
- There is systolic dysfunction with an average LVEF of 33%
- It is notable that there is hypokinesis in both the noncompacted as well as the compacted segments. It has been speculated that this is due to the microcirculatory defect observed in these patients.
- There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictive filling pattern.
- The left ventricular wall is thick with a two layered appearance
- The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick
- The ratio of the non-compacted endocardial layer to the epicardial layer is > 2 in adults and >1.4 in children
- 41% of patients will have involvement of the RV apex
References
- ↑ Weiford BC, Subbarao VD, Mulhern KM, Noncompaction of the ventricular myocardium. Circulation 109 (24): 2965-71 2004
- ↑ .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.