Pulmonary hypertension causes: Difference between revisions
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(By Classes, Dana Point 2008) | |||
Class 1: Pulmonary Aterial Hypertension | |||
#Idiopathic PAH | #Idiopathic PAH | ||
#Heritable( BMPR2,ALK-1,Endogin...) | #Heritable( BMPR2,ALK-1,Endogin...) | ||
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#Persistent Pulmonary Hypertension of the newborn | #Persistent Pulmonary Hypertension of the newborn | ||
Class 2: Pulmonary Venous Hypertension or pulmonary hypertension owing to left heart disease | |||
#Systolic Dysfunction. | #Systolic Dysfunction. | ||
#Diastolic dysfunction. | #Diastolic dysfunction. | ||
#Valvular disease. | #Valvular disease. | ||
Class 2: Pulmonary Hypertension associated with disorders of the respiratory system and/or Hypoxemia | |||
#Chronic Obstructive Pulmonary Disease. | #Chronic Obstructive Pulmonary Disease. | ||
#Interstitial Lung Disease | #Interstitial Lung Disease | ||
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#Developmental abnormalities. | #Developmental abnormalities. | ||
Class 4: Pulmonary Hypertension due to chronic thrombotic and/or embolic disease | |||
Class 5: Pulmonary Hypertension due to disorders directly affecting the pulmonary vasculature | |||
#Hematologic disorders: Myeloproliferative disorders,splenectomy,polycythemia vera. | #Hematologic disorders: Myeloproliferative disorders,splenectomy,polycythemia vera. | ||
#Systemic disorders: Sarcoidosis,Langerhan cell Histiocytosis, Neurofibromatosis, Vasculitis. | #Systemic disorders: Sarcoidosis,Langerhan cell Histiocytosis, Neurofibromatosis, Vasculitis. | ||
#Metabolic disorders: Glycogen storage diseases, Gaucher disease, Thyroid disorders. | #Metabolic disorders: Glycogen storage diseases, Gaucher disease, Thyroid disorders. | ||
#Miscellaneous: Tumor obstruction, Fibrosing mediastinitis, chronic renal failure on dialysis. | #Miscellaneous: Tumor obstruction, Fibrosing mediastinitis, chronic renal failure on dialysis. |
Revision as of 14:17, 8 September 2011
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Differential Diagnosis of the causes of Pulmonary Hypertension
(In Alphabetical Order)
- Alveolar capillary dysplasia with misalignment of pulmonary veins
- Atrial Septal Defects
- Altitude sickness, chronic
- Bronchiectasis
- Bronchopulmonary Dysplasia
- Cholesterol ester storage disease
- Chronic obstructive pulmonary disease
- Cor triatriatum
- Cystic fibrosis
- Churg-Strauss syndrome
- Coal worker pneumoconiosis
- Chronic renal failure on dialysis
- Chronic hemolytic anemia
- Diastolic left heart dysfunction
- Diethylpropion
- Eisenmenger syndrome
- Fallot tetralogy
- Fetal circulation, persistent
- Fibrosing mediastinitis
- Gaucher disease
- Glycogen storage diseases
- Idiopathic pulmonary haemosiderosis
- Idiopathic spinal scoliosis
- Indian familial childhood cirrhosis
- Interstitial Lung Disease
- Langerhan cell Histiocytosis
- Mitral valve incompetence
- Mitral valve stenosis
- Monocrotaline poisoning
- Myeloproliferative disorders
- Neurofibromatosis
- Obstructive sleep apnoea
- Pulmonary alveolar microlithiasis
- Pickwickian syndrome
- Paroxysmal nocturnal haemoglobinuria
- Portal hypertension
- Polycythemia vera
- Pulmonary fibrosis
- Pulmonary embolism
- Pulmonary veno-occlusive disease
- Pulmonary capillary hemangiomatosis
- Phentermine poisoning
- Primary pulmonary hypertension
- Sarcoidosis
- Schistosoma japonicum
- Schistosoma mansoni
- Splenectomy
- Systemic lupus erythematosus
- Systolic Left heart dysfunction
- Tropical pulmonary eosinophilia
- Vasculitis
- Ventricular septal defect
- Ventricular septal defect
(By Classes, Dana Point 2008)
Class 1: Pulmonary Aterial Hypertension
- Idiopathic PAH
- Heritable( BMPR2,ALK-1,Endogin...)
- Drug and toxin induced.
- Connective tissue diseases
- HIV
- Portal Hypertension
- Congenital heart diseases
- Schistosomiasis
- Chronic hemolytic anemia.
- Persistent Pulmonary Hypertension of the newborn
Class 2: Pulmonary Venous Hypertension or pulmonary hypertension owing to left heart disease
- Systolic Dysfunction.
- Diastolic dysfunction.
- Valvular disease.
Class 2: Pulmonary Hypertension associated with disorders of the respiratory system and/or Hypoxemia
- Chronic Obstructive Pulmonary Disease.
- Interstitial Lung Disease
- Pulmonary diseases with mixed restrictive and obstructive patterns.
- Obstructive sleep apnea.
- High Altitude(chronically).
- Developmental abnormalities.
Class 4: Pulmonary Hypertension due to chronic thrombotic and/or embolic disease
Class 5: Pulmonary Hypertension due to disorders directly affecting the pulmonary vasculature
- Hematologic disorders: Myeloproliferative disorders,splenectomy,polycythemia vera.
- Systemic disorders: Sarcoidosis,Langerhan cell Histiocytosis, Neurofibromatosis, Vasculitis.
- Metabolic disorders: Glycogen storage diseases, Gaucher disease, Thyroid disorders.
- Miscellaneous: Tumor obstruction, Fibrosing mediastinitis, chronic renal failure on dialysis.