Pulmonary hypertension causes: Difference between revisions

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(By Classes, Dana Point 2008)
 
Class 1: Pulmonary Aterial Hypertension
 
 
==Class 1: Pulmonary Aterial Hypertension==
#Idiopathic PAH
#Idiopathic PAH
#Heritable( BMPR2,ALK-1,Endogin...)
#Heritable( BMPR2,ALK-1,Endogin...)
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#Persistent Pulmonary Hypertension of the newborn
#Persistent Pulmonary Hypertension of the newborn


==Class 2: Pulmonary Venous Hypertension or pulmonary hypertension owing to left heart disease==
Class 2: Pulmonary Venous Hypertension or pulmonary hypertension owing to left heart disease
#Systolic Dysfunction.
#Systolic Dysfunction.
#Diastolic dysfunction.
#Diastolic dysfunction.
#Valvular disease.
#Valvular disease.


==Class 2: Pulmonary Hypertension associated with disorders of the respiratory system and/or Hypoxemia==
Class 2: Pulmonary Hypertension associated with disorders of the respiratory system and/or Hypoxemia
#Chronic Obstructive Pulmonary Disease.
#Chronic Obstructive Pulmonary Disease.
#Interstitial Lung Disease
#Interstitial Lung Disease
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#Developmental abnormalities.
#Developmental abnormalities.


==Class 4: Pulmonary Hypertension due to chronic thrombotic and/or embolic disease==
Class 4: Pulmonary Hypertension due to chronic thrombotic and/or embolic disease


==Class 5: Pulmonary Hypertension due to disorders directly affecting the pulmonary vasculature==
Class 5: Pulmonary Hypertension due to disorders directly affecting the pulmonary vasculature
#Hematologic disorders: Myeloproliferative disorders,splenectomy,polycythemia vera.
#Hematologic disorders: Myeloproliferative disorders,splenectomy,polycythemia vera.
#Systemic disorders: Sarcoidosis,Langerhan cell Histiocytosis, Neurofibromatosis, Vasculitis.
#Systemic disorders: Sarcoidosis,Langerhan cell Histiocytosis, Neurofibromatosis, Vasculitis.
#Metabolic disorders: Glycogen storage diseases, Gaucher disease, Thyroid disorders.
#Metabolic disorders: Glycogen storage diseases, Gaucher disease, Thyroid disorders.
#Miscellaneous: Tumor obstruction, Fibrosing mediastinitis, chronic renal failure on dialysis.
#Miscellaneous: Tumor obstruction, Fibrosing mediastinitis, chronic renal failure on dialysis.

Revision as of 14:17, 8 September 2011

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Differential Diagnosis of the causes of Pulmonary Hypertension

(In Alphabetical Order)


(By Classes, Dana Point 2008) Class 1: Pulmonary Aterial Hypertension

  1. Idiopathic PAH
  2. Heritable( BMPR2,ALK-1,Endogin...)
  3. Drug and toxin induced.
  4. Connective tissue diseases
  5. HIV
  6. Portal Hypertension
  7. Congenital heart diseases
  8. Schistosomiasis
  9. Chronic hemolytic anemia.
  10. Persistent Pulmonary Hypertension of the newborn

Class 2: Pulmonary Venous Hypertension or pulmonary hypertension owing to left heart disease

  1. Systolic Dysfunction.
  2. Diastolic dysfunction.
  3. Valvular disease.

Class 2: Pulmonary Hypertension associated with disorders of the respiratory system and/or Hypoxemia

  1. Chronic Obstructive Pulmonary Disease.
  2. Interstitial Lung Disease
  3. Pulmonary diseases with mixed restrictive and obstructive patterns.
  4. Obstructive sleep apnea.
  5. High Altitude(chronically).
  6. Developmental abnormalities.

Class 4: Pulmonary Hypertension due to chronic thrombotic and/or embolic disease

Class 5: Pulmonary Hypertension due to disorders directly affecting the pulmonary vasculature

  1. Hematologic disorders: Myeloproliferative disorders,splenectomy,polycythemia vera.
  2. Systemic disorders: Sarcoidosis,Langerhan cell Histiocytosis, Neurofibromatosis, Vasculitis.
  3. Metabolic disorders: Glycogen storage diseases, Gaucher disease, Thyroid disorders.
  4. Miscellaneous: Tumor obstruction, Fibrosing mediastinitis, chronic renal failure on dialysis.