Lung agenesis: Difference between revisions
| Line 11: | Line 11: | ||
==Pathophysiology== | ==Pathophysiology== | ||
On the affected side, the pleural cavity is absent, and the healthy lung occupies the entire thorax. | On the affected side, the pleural cavity is absent, and the healthy lung occupies the entire thorax. | ||
===Associated | ===Associated Conditions=== | ||
*[[Truncus arteriosus]] | *[[Truncus arteriosus]] <ref name="pmid11051161">{{cite journal | author = Krivchenya DU, Dubrovin AG, Krivchenya TD, Khursin VN, Lysak CV | title = Aplasia of the right lung in a 4-year-old child: surgical stabilization of the mediastinum by diaphragm translocation leading to complete recovery from respiratory distress syndrome | journal = Journal of Pediatric Surgery | volume = 35 | issue = 10 | pages = 1499–502 | year = 2000 | month = October | pmid = 11051161 | doi = 10.1053/jpsu.2000.16424 | url = http://linkinghub.elsevier.com/retrieve/pii/S0022-3468(00)55743-1 | issn = | accessdate = 2012-09-16}}</ref> | ||
==Epidemiology and Demographics== | ==Epidemiology and Demographics== | ||
Revision as of 13:49, 16 September 2012
|
WikiDoc Resources for Lung agenesis |
|
Articles |
|---|
|
Most recent articles on Lung agenesis Most cited articles on Lung agenesis |
|
Media |
|
Powerpoint slides on Lung agenesis |
|
Evidence Based Medicine |
|
Clinical Trials |
|
Ongoing Trials on Lung agenesis at Clinical Trials.gov Trial results on Lung agenesis Clinical Trials on Lung agenesis at Google
|
|
Guidelines / Policies / Govt |
|
US National Guidelines Clearinghouse on Lung agenesis NICE Guidance on Lung agenesis
|
|
Books |
|
News |
|
Commentary |
|
Definitions |
|
Patient Resources / Community |
|
Patient resources on Lung agenesis Discussion groups on Lung agenesis Patient Handouts on Lung agenesis Directions to Hospitals Treating Lung agenesis Risk calculators and risk factors for Lung agenesis
|
|
Healthcare Provider Resources |
|
Causes & Risk Factors for Lung agenesis |
|
Continuing Medical Education (CME) |
|
International |
|
|
|
Business |
|
Experimental / Informatics |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Lung agenesis is defined as partial or complete failure of the lung to form with absence of the lung parenchyma, the bronchus and the pulmonary vessels.
Classification
The condition can be unilateral (compatible with life) or bilateral (fatal).
Pathophysiology
On the affected side, the pleural cavity is absent, and the healthy lung occupies the entire thorax.
Associated Conditions
Epidemiology and Demographics
Lung agenesis is extremely rare.
Natural History, Complications, Prognosis
Natural History
The natural history is variable.
Complications
There can be kinking of the trachea and compression of the trachea.
Prognosis
Although 50% of patients may die before the age of 5, the remainder of the individuals may be asymptomatic throughout their lives. Bilateral lung agenesis is a lethal anomaly.
References
- ↑ Krivchenya DU, Dubrovin AG, Krivchenya TD, Khursin VN, Lysak CV (2000). "Aplasia of the right lung in a 4-year-old child: surgical stabilization of the mediastinum by diaphragm translocation leading to complete recovery from respiratory distress syndrome". Journal of Pediatric Surgery. 35 (10): 1499–502. doi:10.1053/jpsu.2000.16424. PMID 11051161. Retrieved 2012-09-16. Unknown parameter
|month=ignored (help)