Sandbox:Sara
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Sara Mohsin, M.D.[2]
- Dermatofibrosarcoma protuberans is estimated to occur in 1 in 100,000 to 1-5 in 1 million people per year
- It usually occurs in adults of 20 - 40 years of age
- It affects twice more commonly the blacks than whites in US[1]
- It can also occur in infants and children[2][3][4]
- It has a stable incidence which is highest among women[5][6]
- Worse survival is associated with:
- ↑ Criscione VD, Weinstock MA (2007). "Descriptive epidemiology of dermatofibrosarcoma protuberans in the United States, 1973 to 2002". J Am Acad Dermatol. 56 (6): 968–73. doi:10.1016/j.jaad.2006.09.006. PMID 17141362.
- ↑ Reddy C, Hayward P, Thompson P, Kan A (2009). "Dermatofibrosarcoma protuberans in children". J Plast Reconstr Aesthet Surg. 62 (6): 819–23. doi:10.1016/j.bjps.2007.11.009. PMID 18096453.
- ↑ Zaraa I, Ben abdallah M, Driss M, Trojjet S, Ben Sassi M, El Euch D; et al. (2011). "[Dermatofibrosarcoma protuberans in children]". Arch Pediatr. 18 (1): 23–7. doi:10.1016/j.arcped.2010.09.010. PMID 20952167.
- ↑ Maire G, Fraitag S, Galmiche L, Keslair F, Ebran N, Terrier-Lacombe MJ; et al. (2007). "A clinical, histologic, and molecular study of 9 cases of congenital dermatofibrosarcoma protuberans". Arch Dermatol. 143 (2): 203–10. doi:10.1001/archderm.143.2.203. PMID 17310000.
- ↑ Kreicher KL, Kurlander DE, Gittleman HR, Barnholtz-Sloan JS, Bordeaux JS (2016). "Incidence and Survival of Primary Dermatofibrosarcoma Protuberans in the United States". Dermatol Surg. 42 Suppl 1: S24–31. doi:10.1097/DSS.0000000000000300. PMID 26730971.
- ↑ Kuzel P, Metelitsa AI, Dover DC, Salopek TG (2012). "Epidemiology of dermatofibrosarcoma protuberans in Alberta, Canada, from 1988 to 2007". Dermatol Surg. 38 (9): 1461–8. doi:10.1111/j.1524-4725.2012.02482.x. PMID 22691126.