Noncompaction cardiomyopathy natural history
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
The presence of NCC is associated with congestive heart failure and disesae in other organs.
Complications and Associated Involvement of Other Organs
Cardiac Disease
- Abnormalities of the origin of the left coronary artery
- Pulmonary atresia
- Pulmonary stenosis
- Right or Left ventricle obstruction
- Hypoplastic left ventricle
- Mitral regurgitation
- Tachyarrhythmias and sudden cardiac death
- Thrombus formation in the left ventricle
Neurologic Complications
Associated Genetic Disorders
Prognosis
In so far as noncompaction cardiomyopathy is a recently described entity, its association with long term clinical outcomes is not known. In a 2005 study [1] which documented the long term follow up of 34 patients who were symptomatic with NCC, 35% had died at the age of 42 +/- 40 months. 12% of the patients required cardiac transplantation due to heart failure.
The prognosis associated with NCC may be better than that reported in this article because only symptomatic patients were included in the aforementioned study. Genetic testing reveals that there are patients with lesser degrees of symptoms, and the prognosis in these patients has not been well defined.
References
- ↑ Oechslin, Erwin; Jenni, Rolf (2005). "Non-compaction of the Left Ventricular Myocardium - From Clinical Observation to the Discovery of a New Disease" (webpage).