Tricuspid atresia surgery
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Tricuspid atresia Microchapters |
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Diagnosis |
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Treatment |
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Special Scenarios |
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Case Studies |
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Tricuspid atresia surgery On the Web |
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American Roentgen Ray Society Images of Tricuspid atresia surgery |
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Risk calculators and risk factors for Tricuspid atresia surgery |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor-In-Chief: Keri Shafer, M.D. [2] Priyamvada Singh, MBBS [[3]]; Assistant Editor-In-Chief: Kristin Feeney, B.S. [[4]]
Overview
Surgery
ACC/AHA 2008 Guidelines - Recommendation for Surgical Options for Patients With Single Ventricle - Tricuspid atresia (DO NOT EDIT)
| Class I |
| "1.Surgeons with training and expertise in congenital heart disease (CHD) should perform operations for single-ventricle anatomy or physiology.(Level of Evidence: C) " |
Surgical Interventions
There are a number of interventional methods to address a tricuspid atresia. These include:
- PGE1 to maintain patent ductus arteriosus
- Modified Blalock-Taussig shunt to maintain pulmonary blood flow by placing a Gortex conduit between the subclavian artery and the pulmonary artery.
- Cavopulmonary anastomosis (hemi-Fontan or bidirectional Glenn) to provide stable pulmonary flow
- Fontan procedure to redirect inferior vena cava and hepatic vein flow into the pulmonary circulation
ACC/AHA Guidelines - Recommendation for Evaluation and Follow-Up After Fontan Procedure (DO NOT EDIT)
| Class I |
| "1.Lifelong follow-up is recommended for patients after a Fontan type of operation; this should include a yearly evaluation by a cardiologist with expertise in the care of adult congenital heart disease (ACHD) patients.(Level of Evidence: C) " |
ACC/AHA Guidelines - Recommendations for Surgery for Adults with Prior Fontan Repair (DO NOT EDIT)
| Class I |
| "1.Surgeons with training and expertise in CHD should perform operations on patients with prior Fontan repair for single-ventricle physiology.(Level of Evidence: C) " |
| "2.Reoperation after Fontan is indicated for the following:(Level of Evidence: C) " |
| "a.Unintended residual atrial septal defect (ASD) that results in right-to-left shunt with symptoms and/or cyanosis not amenable to transcatheter closure.(Level of Evidence: C) " |
| "b.Hemodynamically significant residual systemic artery-to-pulmonary artery shunt, residual surgical shunt, or residual ventricle-to-pulmonary artery connection not amenable to transcatheter closure.(Level of Evidence: C) " |
| "c.Moderate to severe systemic atrioventricular (AV) valve regurgitation.(Level of Evidence: C) " |
| "d.Significant (greater than 30-mm Hg peak-to-peak) subaortic obstruction.(Level of Evidence: C) " |
| "e.Fontan pathway obstruction.(Level of Evidence: C) " |
| "f.Development of venous collateral channels or pulmonary arteriovenous malformation not amenable to transcatheter management.(Level of Evidence: C) " |
| "g.Pulmonary venous obstruction.(Level of Evidence: C) " |
| "h.Rhythm abnormalities, such as complete AV block or sick sinus syndrome, that require epicardial pacemaker insertion.(Level of Evidence: C) " |
| "i.Creation or closure of a fenestration not amenable to transcatheter intervention.(Level of Evidence: C) " |
| Class IIa |
| "1.Reoperation for Fontan conversion (i.e., revision of an atriopulmonary connection to an intracardiac lateral tunnel, intra-atrial conduit, or extracardiac conduit) can be useful for recurrent atrial fibrillation or flutter without hemodynamically significant anatomic abnormalities. A concomitant Maze procedure should also be performed.(Level of Evidence: C) " |
| Class IIb |
| "1.Heart transplantation may be beneficial for severe SV dysfunction or protein-losing enteropathy (PLE).(Level of Evidence: C) " |