Lutembacher's syndrome
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor-in-Chief: Ayokunle Olubaniyi, M.B,B.S
Overview
Lutembacher's syndrome is a rare form of congenital heart disease. It refers to a combination of congenital atrial septal defect complicated by an acquired mitral stenosis. The atrial septal defect is usually a specific type called a secundum atrial septal defect.
Epidemiology and Demographics
This is a very rare disease. The incidence is 0.001/1000000[1].
Complications and Prognosis
Complications are usually related to a late diagnosis. They include pulmonary hypertension and heart failure. Early diagnosis and surgical treatment has a good prognostic value.
Diagnosis
History and Symptoms
Physical Examination
Chest X Ray
Echocardiography
Treatment
Medical Therapy
Surgery
References
- ↑ Berry NS, Bauman JL, Gallastegui JL, Bauma W, Beckman KJ, Hariman RJ (1988). "Analysis of antiarrhythmic drug concentrations determined during electrophysiologic drug testing in patients with inducible tachycardias". Am J Cardiol. 61 (11): 922–4. PMID 3354470.