Malignant rhabdoid tumor

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]Associate Editor(s)-in-Chief: Sujit Routray, M.D. [2]

Overview

• Malignant rhabdoid tumor is one of the aggressive tumors in the pediatric population. It was originally described as a rhabdomyosarcomatoid variant of Wilms' tumor, which is primarily a kidney tumor.
• Malignant rhabdoid tumor was first described as a variant of Wilms' tumor of the kidney, in 1978.
• Later, rhabdoid tumours outside the kidney were reported in many tissues including the liver, soft tissue, and the central nervous system.
• Malignant rhabdoid tumor of the kidney is a rare malignancy, closely related to atypical teratoid rhabdoid tumor of the brain.