Desmoplastic small round cell tumor
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]Associate Editor(s)-in-Chief: Sujit Routray, M.D. [2]
Synonyms and keywords: Desmoplastic small round cell tumour; Desmoplastic small round blue cell tumor; Desmoplastic small round blue cell tumour; Intraabdominal desmoplastic small round blue cell tumor; Desmoplastic small cell tumor; Desmoplastic cancer; Desmoplastic sarcoma; DSRCT
Overview
Desmoplastic small round cell tumor is a rare but highly fatal malignancy.[1]
Historical Perspective
Desmoplastic small round cell tumor was first discovered by pathologists, William L. Gerald and Juan Rosai, in 1989.[2]
Classification
Pathophysiology
Causes
Differentiating Desmoplastic Small Round Cell Tumor from other Diseases
Epidemiology and Demographics
=Incidence
Age-adjusted incidence rate for African Americans and Caucasians is 0.05 and 0.02 per 100,000 individuals, respectively.[1]
Age
Peak age of incidence for desmoplastic small round cell tumor is between 20 and 24 years.[1]
Risk Factors
There are no established risk factors for desmoplastic small round cell tumor.[3]
Screening
Natural History, Complications, and Prognosis
Diagnosis
History and Symptoms
Physical Examination
Laboratory Findings
X Ray
CT
MRI
Ultrasound
Other Imaging Findings]
Other Diagnostic Studies
Treatment
Medical Therapy
Surgery
Primary Prevention
Secondary Prevention
References
- ↑ 1.0 1.1 1.2 Lettieri, Christina K.; Garcia-Filion, Pamela; Hingorani, Pooja (2014). "Incidence and Outcomes of Desmoplastic Small Round Cell Tumor: Results from the Surveillance, Epidemiology, and End Results Database". Journal of Cancer Epidemiology. 2014: 1–5. doi:10.1155/2014/680126. ISSN 1687-8558.
- ↑ Pathology of desmoplastic small round cell tumor. Wikipedia 2016. https://en.wikipedia.org/wiki/Desmoplastic_small-round-cell_tumor. Accessed on March 29, 2016
- ↑ Causes of desmoplastic small round cell tumor. Wikipedia 2016. https://en.wikipedia.org/wiki/Desmoplastic_small-round-cell_tumor. Accessed on March 29, 2016