11β-hydroxylase deficiency surgery

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Congenital adrenal hyperplasia main page

Overview

Classification

21-hydroxylase deficiency
11β-hydroxylase deficiency
17 alpha-hydroxylase deficiency
3 beta-hydroxysteroid dehydrogenase deficiency
Cytochrome P450-oxidoreductase (POR) deficiency (ORD)
Lipoid congenital adrenal hyperplasia

Differential Diagnosis

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Mehrian Jafarizade, M.D [2]

Overview

Girls with ambiguous genitalia mostly undergo reconstructive surgery such as clitoroplasty and vaginoplasty. In clitoral reduction surgery neurovascular bundle, the glans, and the preputial skin related to the glans should be kept completely.

Surgery

Girls with ambiguous genitalia mostly undergo reconstructive surgery such as clitoroplasty and vaginoplasty. In clitoral reduction surgery neurovascular bundle, the glans, and the preputial skin related to the glans should be kept completely.[1][2]

References

  1. Premawardhana LD, Hughes IA, Read GF, Scanlon MF (1997). "Longer term outcome in females with congenital adrenal hyperplasia (CAH): the Cardiff experience". Clin Endocrinol (Oxf). 46 (3): 327–32. PMID 9156043.
  2. Hendren WH, Donahoe PK (1980). "Correction of congenital abnormalities of the vagina and perineum". J. Pediatr. Surg. 15 (6): 751–63. PMID 7007606.