Ebstein's anomaly of the tricuspid valve
| Ebstein's anomaly of the tricuspid valve | |
 | |
|---|---|
| Chest X-ray of a patient with Ebstein's anomaly Image courtesy of RadsWiki | |
| ICD-10 | Q22.5 |
| ICD-9 | 746.2 |
| OMIM | 224700 |
| DiseasesDB | 4039 |
| eMedicine | med/627 |
| MeSH | D004437 |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] and Claudia P. Hochberg, M.D. [2]
Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [3]
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Overview
Etymology
Ebstein's anomaly was named after Wilhelm Ebstein.[1][2]
Diagnoses Ebstein's Anomaly of the Tricuspid Valve should be Distinguished from
- Accessory pathway-mediated WPW syndrome and SVT
- Atrial septal defect (ASD)
- Cyanotic congenital heart diseases
- Isolated, severe tricuspid regurgitation
- L-transposition of the great vessels
- Severe right heart failure
Associated Abnormalities
Epidemiology and demographics
Genetics
- Multifactorial inheritance, risk if a sibling has the disease is 1%.
Diagnosis
History | Physical examination | Laboratory findings | CT and MRI
Treatment
Prognosis
References
- ↑ Template:WhoNamedIt
- ↑ W. Ebstein. Über einen sehr seltenen Fall von Insufficienz der Valvula tricuspidalis, bedingt durch eine angeborene hochgradige Missbildung derselben. Archiv für Anatomie, Physiologie und wissenschaftliche Medicin, Leipzig, 1866, 238-254.
Additional Resources
- Emma C. Ferguson, Rajesh Krishnamurthy, and Sandra A. A. Oldham. Classic Imaging Signs of Congenital Cardiovascular Abnormalities. RadioGraphics 2007 27: 1323-1334.
- Joris P. A. Beerepoot, and Pamela K. Woodard. Case 71: Ebstein Anomaly. Radiology 2004 231: 747-751.