Noncompaction cardiomyopathy echocardiography
|
Noncompaction Cardiomyopathy Microchapters |
|
Pathophysiology |
|---|
|
Differentiating Noncompaction Cardiomyopathy from other Diseases |
|
Diagnosis |
|
Treatment |
|
Noncompaction cardiomyopathy echocardiography On the Web |
|
Risk calculators and risk factors for Noncompaction cardiomyopathy echocardiography |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
On echocardiography there is ventricular hypertrophy with deep recesses which tend to be located apically [1].
Echocardiographic findings
- There are deep trabeculations in the ventricular wall
- There is systolic dysfunction with an average LVEF of 33% [2]
- There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictie filling pattern[3].
- The left ventricular wall is thick with a two layered appearance
- The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick
- The ratio of the non-compacted endocardial layer to the epicardial layer is > 2 in adults and >1.4 in children
- 41% of patients will have involvement of the RV apex [4]
References
- ↑ Weiford BC, Subbarao VD, Mulhern KM, Noncompaction of the ventricular myocardium. Circulation 109 (24): 2965-71 2004
- ↑ .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.
- ↑ .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.
- ↑ .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.