Cardiac disease in pregnancy and marfan's syndrome
Cardiac disease in pregnancy Microchapters |
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]
Overview
- Autosomal dominant inheritance pattern (counseling is essential)
- Major risk is aortic dissection
- Most common in 3rd trimester or 1st stage of labor
- Increases with enlarging aortic root diameter
- Prophylactic beta-blockers appear to be helpful
- Close follow-up with serial echocardiography
- Surgery:
- Surgery recommended pre-conception if root diameter >40 mm
- Surgery recommend during gestation if > 55 mm