Bickers-Adams syndrome
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Bickers-Adams syndrome is a rare aex-linked cause of hydrocephalus due to aqueductal stenosis.
Diagnosis
Physical Examination
mental deficiency, and flexion deformities and spasticity of the extremities. HSAS, MASA (mental retardation, adducted thumbs, shuffling gait, and aphasia), and complicated paraplegia (SPG1) share many common characteristics. Later studies reported HSAS patients with hydrocephalus but without aqueductal stenosis.