Sandbox: DDx Kidney mass
- 3-4 yo patients
- Asymptomatic abdominal mass
- May have abdominal pain, fever, nausea/vomiting, hematuria, and hypertension
- Beckwith-Wiedemann syndrome and WAGR syndrome
- Unilateral, smooth, firm, nontender, flank mass
- Does not cross the midline
- WT1 and WT2 genes on chromosome 11
- WTX gene on chromosome X
Nonmalignant causes
anaplastic sarcoma clear cell sarcoma mesoblastic nephroma metanephric stromal tumor nephroblastomatosis / nephrogenic rests neuroblastoma oncocytoid carcinoma after neuroblastoma ossifying tumor renal cell carcinoma rhabdoid tumor translocation carcinoma (children) Wilms tumor of children